This chapter discusses tumours of nose and PNS, where congenital tumours of nose may be seen externally or inside the nasal cavity due to a defect in foramen caecum. Gliomas are solid masses consisting of neuroglial tissue and astrocytes. Encephalocele is herniation of dura mater in the nose through foramen caecum or a defect in cribriform plate of ethmoid. Fibromas and neurofibromas arise from fibrous tissue and nerves of the nasal cavity and may form polypoidal masses. Sarcomas are commonly seen tumour of nose and it may be fibrosarcoma, myxosarcoma and rhabdomyosarcoma. Dermoid cyst may be seen in midline on dorsum of nose, contains hair and amorphous material and may have a sinus opening on the surface. Osteomas mostly arise from frontal, ethmoidal or maxillary sinus. Squamous cell carcinoma is seen mostly in nickel workers while adenocarcinoma in wood workers. Polytomography is better than plain X-ray because it demonstrates better details of destruction.