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Chapter-35 Pseudomyxoma Peritonei

BOOK TITLE: Ovarian Cancer: Comprehensive and Contemporary Management

Author
1. Peedicayil Abraham
ISBN
9788184485394
DOI
10.5005/jp/books/10583_35
Edition
1/e
Publishing Year
2009
Pages
7
Author Affiliations
Chapter keywords

Abstract

PMP is a rare mucinous neoplasm affecting the peritoneal surfaces and giving rise to the syndrome of “jelly belly”. It is more common in women and is associated with mucinous tumours of the appendix and ovary. Patients present with abdominal distension and non-specific symptoms with signs of non-shifting ascites. The diagnosis is usually made only at laparotomy. There are three pathological types: disseminated peritoneal adenomucinosis, borderline peritoneal mucinous carcinomatosis and peritoneal mucinous carcinomatosis. Treatment approaches include serial debulking, cytoreductive surgery followed by adjuvant radiation or chemotherapy and peritonectomy followed by hyperthermic intraperitoneal chemotherapy. Although an indolent disease there is eventual bowel obstruction. The 10 year overall survival is 80% with aggressive treatment (Sugarbaker technique) however this can be quite toxic and should be undertaken only in specialized centres.

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