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Chapter-09 Coats' Disease

BOOK TITLE: Manual of Ocular Pathology

Author
1. Biswas Jyotirmay
2. Krishnakumar S
3. Ahuja Shweta
ISBN
9788184489125
DOI
10.5005/jp/books/11243_9
Edition
1/e
Publishing Year
2010
Pages
2
Author Affiliations
1. Sankara Nethralaya, Chennai, Tamil Nadu, India, Sankara Nethralaya, Chennai, Tamil Nadu, Ind, Sankara Nethralaya, A Unit of Medical Research Foundation, Nungambakkam, Chennai, Tamil Nadu, India, Sankara, Nethralaya, Chennai, Tamil Nadu, India, Medical Research Foundation, Sankara Nethralaya, Chennai, India, Sankara Nethralaya, Chennai, India, Medical and Vision Research Foundation, Shankara Nethralaya, Chennai, Medical and Vision Research Foundations, Chennai, Tamil Nadu, India, Medical and Vision Research Foundation Sankara Nethralaya, 18, College Road Chennai, India, Sankara Nethralaya, Medical and Vision Research Foundation, Chennai, India
2. Medical and Vision Research Foundations Sankara Nethralaya, 18, College Road, Chennai, India, Sankara Nethralaya, Chennai, India, Kumars’ Maternity and Surgical Nursing Home, Dombivli, Nirmiti Fertility and IVF Center, Thane, Fortis Hospitals, Mumbai, Maharashtra, India, Mumbai, Maharashtra, India, IAGE, ISAR; JK Women Hospital Mumbai, Maharashtra, India, IAGE, ISAR, JK Women Hospital, Mumbai, Maharashtra, India
3. Medical and Vision Research Foundations Sankara Nethralaya, 18, College Road, Chennai, India
Chapter keywords

Abstract

A histopathological definition of Coat’s disease is inclusive of criteria such as architecture of vasculature, degeneration of the retina and other such pathognomonic features. A differentiation from other causes of leukocoria is crucial as this is a disease that is known to most frequently affect boys in their first decade and could be mistaken for retinoblastoma. Histopathology of the enucleated globe reveals exudative retinal detachment, retinal oedema, and cystic degeneration of the retina, telangiectatic retinal vessels, lipid laden macrophages and cholesterol clefts.

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