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Chapter-69 Management of Retinitis Pigmentosa and other Disorders

BOOK TITLE: Surgical Techniques in Ophthalmology (Pediatric Ophthalmic Surgery)

Author
1. Aurora Ajay
2. Sanduja Neeraj
ISBN
9789350251485
DOI
10.5005/jp/books/11282_69
Edition
1/e
Publishing Year
2011
Pages
22
Author Affiliations
1. Delhi Retina Centre, Chaudhary Eye Centre and Laser Vision, 4802, Bharat Ram Road 24, Darya Ganj, New Delhi, India, Delhi Retina Centre, Chaudhary Eye Centre and Laser, Vision, Bharat Ram Road, 24, Darya Ganj, New Delhi, India, Delhi Retina Centre, Chaudhary Eye Centre and Laser Vision, 4802, Bharat Ram Road, 24, Darya Ganj, New Delhi, India, Delhi Retina Centre, Chaudhary Eye Centre and Laser Vision, 4802, New Delhi, India, Retina-Clinic, Dr. Chaudhary Eye Centre and Laser Vision, 4802 Bharat Ram Road, 24, Daryaganj, New Delhi, India, Delhi Retina Centre, Chaudhary Eye Centre and Laser, Vision, 4802, Bharat Ram Road, 24, Darya Ganj, New Delhi, India, Delhi Retina Centre, Chaudhary Eye Centre and Laser Vision, 4802, Bharat Ram Road 24, Darya Ganj, New Delhi India
2. Dr Chaudhary Eye Centre and Laser Vision, 4802, Bharat Ram Road, 24, Daryaganj, New Delhi, India, Dr. Chaudhary Eye Centre and Laser Vision, 4802, Bharat Ram Road, 24 Daryaganj, New Delhi, India, Dr. Chaudhary Eye Centre and Laser Vision, 4802, Bharat Ram Road, 24, Daryaganj, New Delhi (India), Delhi Retina Centre, 4802 Bharat Ram Road, 24, Daryaganj, New Delhi, India, Delhi Retina Centre, Dr Chaudhary Eye Centre and Laser Vision 4802, Bharat Ram Road 24, Daryaganj, New Delhi, India, Sankara Nethralaya; Michigan, USA; Delhi Retina Center, New Delhi, India
Chapter keywords

Abstract

Retinitis pigmentosa (RP) is a generic term used for a group of disorders that are characterized by progressive destruction of the photoreceptors and the retinal pigment epithelium which in turn damage the inner retinal layers. These patients initially present with night blindness and varying degrees of loss of field. The visual loss gradually advances. It is a genetic dystrophy. Night blindness and slowly, progressive loss of visual field are hallmarks of this disorder. About 35% of all RP patients experience flashes of light that usually occur in the mid peripheral field adjacent to the areas of scotomas, are continuous in nature (those that are associated with migraine are episodic) and usually disappear with advancing disease and enlarging scotomas. The investigations are done through fundus examination, Fluorescein angiography. Cataract and glaucoma are the common complications that are usually found in RP. Visual field assessment is an important aspect of the management of RP. Visual field is able to quantify the affected patient’s visual deficit. Retinal densitometry and dark adaptometry is also used in investigations. There is various classification of Retinitis pigmentosa like on the basis of onset, on the mode of inheritance, etc. Most RP patients are not associated with manifestations outside the eye. About one third of RP patients experience hearing loss of varying degrees as adults. It is not known how many of these are cases of Ushers syndrome as in many cases it is a coincidental association. Patients of RP have a greater than normal risk of thyroid disease. Night vision aid, tinted glasses, cataract surgery are treatment options. Vitamin A supplements and Lutein Supplements are also used.

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