This chapter provides an overview of rare group of brain tumors. They are rare tumors in children and the young adults and have both glial and neuronal elements. They are grouped as a surgically curable cause of intractable seizures. They mimic low-grade gliomas radiologically. Gangliogliomas is the most common; they are granular appearance on imaging. The DNET is nodular. The DIGs are rare surfacing supratentorial with cysts, detected in infants with macrocrania. Immunohistochemistry helps in diagnosis. Surgery is the primary treatment. Role of radiotherapy is controversial. Paraganglioma of filum terminale may mimic an ependymoma. Overall prognosis is favorable.