Chapter-33 Storage Diseases of the Reticuloendothelial System
BOOK TITLE: Practical Pediatric Hematology
Author
1. Moulik Nirmalya Roy
2. Kumar Archana
ISBN
9789350259214
DOI
10.5005/jp/books/11659_16
Edition
2/e
Publishing Year
2012
Pages
8
Author Affiliations
1.
Chhatrapati Shahuji Maharaj Medical University, Lucknow, Uttar Pradesh, India
2.
Chhatrapati Shahuji Maharaj Medical University, Lucknow, Uttar Pradesh, India
Chapter keywords
lysosomal storage diseases (LSDs),
genetic defects,
lysosomal accumulation of substrates,
organ damage,
reticuloendothelial (RE) system,
cytopenias,
hepatosplenomegaly,
lymphadenopathy,
lysosomal storage disorders