In this chapter nine anterior corneal dystrophies have been discussed namely, epithelial basement membrane dystrophy (EBMD), epithelial recurrent erosion dystrophy (ERED), subepithelial mucinous corneal dystrophy (SMCD), Meesmann corneal dystrophy (MECD), Lisch epithelial corneal dystrophy (LECD), gelatinous drop-like corneal dystrophy (GDLD), Reis-Buckler’s corneal dystrophy (RBCD), Thiel-Behnke corneal dystrophy (TBCD) and Grayson-Wilbrandt corneal dystrophy (GWCD). EBMD is the most common anterior corneal dystrophy and the lesions may be unilateral, bilateral and bilaterally asymmetric. ERED presents with bilateral symptomatic corneal erosions. SMCD presents with recurrent bilateral corneal erosions progressing to vision loss. MECD is a bilaterally symmetric, autosomal dominant disorder. LECD presents with unilateral and bilateral gray granular opacities in a band-shaped pattern with whorled and feathery borders. GDLD is characterized by multiple coalescing gelatinous deposits just below the corneal epithelium. RBCD is a bilaterally symmetric which involves the central corneal axis. TBCD presents with central bilateral subepithelial reticular opacities. The GWCD causes loss of vision due to corneal surface irregularity.