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Chapter-17 Thalassemia Syndromes

BOOK TITLE: Textbook of Pediatric Hematology & Hemato-Oncology

Author
1. Lokeshwar MR
2. Sharma Ratna
3. Pandrowala Ambreen
4. Manglani Mamta Vijay
ISBN
9789351521433
DOI
10.5005/jp/books/12680_18
Edition
1/e
Publishing Year
2016
Pages
27
Author Affiliations
1. 19/54, Welfare Mansion, Sion, Mumbai, Lilavati Hospital and Research Centre, Mumbai, Maharashtra; Shushrusha Citizens Cooperative, Hospital Ltd, Mumbai, Maharashtra, LTMG Hospital and Medical College; and Shushrusha Citizens Cooperative Hospital Ltd. Lilavati Hospital and Research Center, Mumbai, Maharashtra, India, Lilavati Hospital and Research Centre, Shushrusha Hospital and Kashyap Clinic, Mumbai, Maharashtra, India, Lilavati Hospital and Research Centre, Shushrusha Citizens’ Co-operative Hospital, Mumbai, Maharashtra, India, Lilavati Hospital, Mumbai; Oncology and Outdoor Thalassemia Transfusion Center, LTM Medical College and LTMG, General Hospital, Mumbai, Maharashtra, India, Lilavati Hospital and Research Centre, Shushrusha Citizens' Co-operative Hospital, Mumbai, Maharashtra, India, Shushrusha Citizens’ Co-operative Hospital Ltd, Mumbai, Lilavati Hospital and Research Center, Mumbai, Maharashtra, P.D. Hinduja National Hospital & Research Center, Mumbai, Imperial Mahal, 3rd Floor, Khodadad Circle,
2. LTMG Hospital and Medical College, Sion, Mumbai, India, Dr DY Patil Hospital, Navi Mumbai, India, PD Hinduja Hospital and Medical Research Centre, Mumbai, Maharashtra, India, Lokmanya Tilak Municipal Medical College and General Hospital, Mumbai; Jupiter Hospital, Mumbai, Maharashtra, India
3. Lilavati Hospital, Mumbai, India
4. Pediatric Center of Excellence for HIV Care, Lokmanya Tilak Municipal Medical College and General Hospital, Mumbai, India, Comprehensive Thalassemia Care Centre and Bone Marrow Transplantation Centre Magathane, Borivli (East), (A Satellite Centre of LTM Medical College and General Hospital, Sion, Mumbai, Maharashtra, India)
Chapter keywords
thalassemia syndromes, transfusion facilities, stem cell transplantation, single gene disorders, globin polypeptide chains, hemoglobin molecule, red cell count, splenomegaly, jaundice, skeletal changes, anemia, hypochromia, microcytosis, target cells, basophilic stippling, reticulocytes, nucleated red cells, osteopenia, osteoporosis, established osteoporosis, human immunodeficiency virus, hypersplenism, gene therapy

Abstract

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