Chapter-46 Hemophagocytic Lymphohistiocytosis: Revisited
BOOK TITLE: Textbook of Pediatric Hematology & Hemato-Oncology
Author
1. Udgire Sunil
2. Desai Mukesh M
ISBN
9789351521433
DOI
10.5005/jp/books/12680_47
Edition
1/e
Publishing Year
2016
Pages
9
Author Affiliations
1.
Bai Jerbai Wadia Hospital, Mumbai, Maharashtra, India,
BJ Wadia Hospital for Children and Institute of Child Health and Research Centre, Mumbai, India,
Sparsh Hospital, Bengaluru, Karnataka, India,
BGS Gleneagles Global Hospital, Bengaluru, Karnataka, India
2.
BJ Wadia Hospital for Children; B Nanavati Hospital, Sir HN Hospital, Saifee Hospital, Asian Heart Institute, India
Chapter keywords
hemophagocytosis lymphohistiocytosis (HLH),
immune dysregulation,
hyperinflammatory syndrome,
pancytopenia,
coagulopathy,
hyperferritinemia,
hypertriglyceridemia,
hemophagocytosis,
NK cells,
cytotoxic T cells