Chronic thromboembolic pulmonary hypertension is a disease due to the presence of unresolved and organized pulmonary thrombi in pulmonary vessels. The clinical features are dyspnea, edema, fatigue, chest pain etc. it is diagnosed by imaging studies like Chest radiograph, V/Q nuclear lung scanning, computed tomography pulmonary angiography etc. CTEPH is potentially curative and the definitive treatment of CTEPH is pulmonary thromboendarterectomy. With the increase in expertise and surgical skills leads to the improvement in the survival and decrease the high mortality. Medically managed patients continue under vigilance over a period of time and may undergo pulmonary arterial hypertension-specific therapies like balloon angioplasty, lung transplantation if needed.