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Section-10 Hematology

BOOK TITLE: IAP Color Atlas of Pediatrics

Author
1. Lokeshwar MR
2. Agarwal Bharat
ISBN
9789351527008
DOI
10.5005/jp/books/12531_11
Edition
2/e
Publishing Year
2015
Pages
38
Author Affiliations
1. 19/54, Welfare Mansion, Sion, Mumbai, Lilavati Hospital and Research Centre, Mumbai, Maharashtra; Shushrusha Citizens Cooperative, Hospital Ltd, Mumbai, Maharashtra, LTMG Hospital and Medical College; and Shushrusha Citizens Cooperative Hospital Ltd. Lilavati Hospital and Research Center, Mumbai, Maharashtra, India, Lilavati Hospital and Research Centre, Shushrusha Hospital and Kashyap Clinic, Mumbai, Maharashtra, India, Lilavati Hospital and Research Centre, Shushrusha Citizens’ Co-operative Hospital, Mumbai, Maharashtra, India, Lilavati Hospital, Mumbai; Oncology and Outdoor Thalassemia Transfusion Center, LTM Medical College and LTMG, General Hospital, Mumbai, Maharashtra, India, Lilavati Hospital and Research Centre, Shushrusha Citizens' Co-operative Hospital, Mumbai, Maharashtra, India, Shushrusha Citizens’ Co-operative Hospital Ltd, Mumbai, Lilavati Hospital and Research Center, Mumbai, Maharashtra, P.D. Hinduja National Hospital & Research Center, Mumbai, Imperial Mahal, 3rd Floor, Khodadad Circle,
2. BJ Wadia Hospital for Children, Mumbai, Maharashtra, BJ Wadia Hospital, Mumbai, Maharashtra, India, Bai Jerbai Wadia Hospital for Children, Institute of Child Health, Mumbai, Maharashtra, Bai Jerbai Wadia Hospital for Children, Parel, Mumbai, Maharashtra, India, Institute of Child Health and Research Center, BJ Wadia Hospital for Children, Mumbai, Maharashtra, India, BJ Wadia Children Hospital, Mumbai, Maharashtra, India, Bai Jerbai Wadia Hospital for Children, Mumbai, Maharashtra, India, BJ Wadia Hospital for Children, Mumbai, Maharashtra, India, Bai Jerbai Wadia Hospital for Children, Mumbai, Maharashtra, BJ Wadia Hospital for Children, Parel, Mumbai, India, BJ Wadia Hospital for Children, Parel, Mumbai, Maharashtra, India
Chapter keywords
hematology, hepatosplenomegaly, pneumococcal vaccine, meningococcal vaccine, hereditary spherocytosis, petechiae, purpura

Abstract

This chapter discusses about the common and uncommon conditions, emergencies, and syndromes in hematology. Most common cause of anemia is due to nutritional deficiencies like iron deficiency, B12, folic acid deficiencies, deficiency of micronutrients particularly when not associated with generalized lymphadenitis or hepatosplenomegaly, petechiae, purpura. Children with hypothyroidism, nephrotic syndrome, CCF look pale without being anemic. Infant with thalassemia major shows no history of consanguinity and increased normoblasts, where mother and father both thalassemia minor. Inadequate treatment leads to growth retardation, pallor, hepatosplenomegaly and organ dysfunction. Malar prominence indicates improper transfusion therapy due to expansion of bone marrow space mainly in flat bones and is due to increased intramedullary erythropoiesis. Hereditary spherocytosis is caused due to recurrent jaundice and mild hepatosplenomegaly, and requires immunization with pneumococcal vaccine, meningococcal vaccine, hib vaccine in addition to routine vaccines.

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