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Chapter-37 Coats' Disease

BOOK TITLE: Retina: Medical and Surgical Management

Author
1. Chawla Rohan
2. Tewari Ruchir
3. Jain Shreyans
ISBN
9789352702947
DOI
10.5005/jp/books/18054_38
Edition
1/e
Publishing Year
2018
Pages
5
Author Affiliations
1. Dr Rajendra Prasad Centre for Ophthalmic Sciences, All India Institute of Medical Sciences, New Delhi, India, Dr RP Center for Ophthalmic Sciences, All India Institute of Medical Sciences, New Delhi, India, RP Centre for Ophthalmic Sciences, AIIMS, New Delhi, Dr Rajendra Prasad Centre for Ophthalmic Sciences, All India Institute of Medial Sciences, New Delhi, India, Dr Rajendra Prasad Centre, All India Institute of Medical Sciences, New Delhi, India, Dr Rajendra Prasad Center for Ophthalmic Sciences, All India Institute of Medical Sciences, New Delhi, India, All India Institute of Medical Sciences, New Delhi, India
2. Dr Rajendra Prasad Centre for Ophthalmic Sciences, All India Institute of Medical Sciences, New Delhi, India, All India Institute of Medical Sciences, New Delhi, India
3. Dr Rajendra Prasad Centre for Ophthalmic Sciences, All India Institute of Medical Sciences, New Delhi, India, All India Institute of Medical Sciences, New Delhi, India
Chapter keywords
Coats’ disease, Norrie disease pseudoglioma, NDP, familial exudative vitreoretinopathy, FEVR, FSHD, capillary nonperfusion, CNP

Abstract

This chapter basically focuses on the coats’ disease. Coats’ disease was first described by a Scottish ophthalmologist George Coats in 1908. it is an idiopathic disorder characterized by aneurysmal and telangiectatic retinal vessels with intraretinal and subretinal exudation and fluid. Exudative retinal detachment is a common feature present in this disease. Coats’ disease is a part of a spectrum of related genetic disorders known as “retinal hypovasculopathies” which consists of Norrie disease, familial exudative vitreoretinopathy (FEVR), fascioscapulohumeral muscular dystrophy (FSHD), and the osteoporosis pseudoglioma syndrome. Usual ophthalmoscopic evaluation is enough for the diagnosis of Coats’ retinopathy, but other disorders need to be ruled out, especially retinoblastoma. Observation and regular follow-up is advised in patients with mild, nonvision threatening disease (stage 1) in which the patient has no symptoms and in those who have end-stage disease with retinal detachment in which visual prognosis is nil. Laser photocoagulation to areas of telangiectasia and CNP should be considered if progressive exudation is documented. Direct laser of leaking vessels can be done under fluorescein guidance.

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