Chapter-03.8 Hepatosplenomegaly in Metabolic Disorders
BOOK TITLE: Differential Diagnosis in Pediatrics
Author
1. Suresh Beena
2. Jagadeesh Sujatha
ISBN
9789352707003
DOI
10.5005/jp/books/18397_27
Edition
1/e
Publishing Year
2020
Pages
9
Author Affiliations
1.
Mediscan Systems, Chennai, Tamil Nadu, India
2.
Mediscan Systems, Chennai, Tamil Nadu, India
Chapter keywords
Hepatosplenomegaly,
metabolic disorder,
imaging technique,
Gaucher disease,
central nervous system,
CNS,
lysosomal storage disorder,
LSD,
skeletal manifestation,
Niemann-pick disease,
GM1-gangliosidosis,
GM2-gangliosidoses,
Sandhoff disease,
Wolman disease,
lysinuric protein