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Chapter-08 Vasculitis and other Vascular Reaction Patterns

BOOK TITLE: IADVL Color Atlas of Dermatopathology

Author
1. Khopkar Uday
2. Nischal KC
3. Khandpur Sujay
4. Mysore Venkataram
5. Mahajan Pradeep
6. Lee Nathan
7. Gardner Jerad
ISBN
9789385891236
DOI
10.5005/jp/books/12981_9
Edition
1/e
Publishing Year
2017
Pages
20
Author Affiliations
1. KEM Hospital and Seth GS Medical, College, Mumbai, Maharashtra, India, KEM Hospital and Seth GS Medical College Mumbai, Seth GS Medical College and KEM Hospital, Mumbai, Maharashtra, India, e-mail: drkhopkar@gmail.com, Seth GS Medical College and KEM Hospital, Mumbai, Maharashtra, India, drkhopkar@gmail.com, Seth GS Medical College and KEM Hospital, Mumbai, Maharashtra, India, KEM Hospital and SGS Medical College, Mumbai, Maharashtra, India, Seth GS Medical College and King Edward Memorial Hospital, Mumbai, India
2. Nirmal Skin and Hair Clinic; Kaya Skin Clinic, Bengaluru, Karnataka, India, Nirmal Skin and Hair Clinic, Bengaluru, Karnataka, India, Adichunchanagiri Institute of Medical Sciences, Bengaluru, Karnataka, India, Adichunchanagiri Institute of Medical Sciences, Bellur, Karnataka, India
3. All India Institute of Medical Sciences, New Delhi, India, All India Institute Medical Science, New Delhi
4. Venkat Charmalaya-centre for Advanced, Dermatology and Postgraduate Training City, Bengaluru, Karnataka, India, Venkat Center for Skin and Plastic Surgery, Bengaluru, Karnataka, India, (Accredited to Rajeev Gandhi University of Health Sciences, Bengaluru), Bengaluru, Karnataka, India
5. Dr Mahajan’s Dermatology and Dermatopathology Services, Pune, Maharashtra, India
6. University of Arkansas for Medical Sciences, Arkansas, USA
7. University of Arkansas for Medical Sciences, Arkansas, USA
Chapter keywords
Leukocytoclastic vasculitis, urticarial vasculitis, polyarteritis nodosa, Wegener’s granulomatosis, Churg-Strauss disease, granuloma faciale, erythema elevatum diutinum, Behcet’s disease, Sweet’s syndrome, pyoderma gangrenosum

Abstract

This chapter focuses on vasculitis and other vascular reaction patterns. The images provided in this chapter are of leukocytoclastic vasculitis, urticarial vasculitis, polyarteritis nodosa, Wegener’s granulomatosis, Churg-Strauss disease, granuloma faciale, erythema elevatum diutinum, Behcet’s disease, Sweet’s syndrome, pyoderma gangrenosum, livedoid vasculitis, pigmented purpuric dermatoses. Leukocytoclastic vasculitis shows IgG deposits, polyarteritis nodosa IgM and Henoch-Schonlein purpura shows IgA deposition in vessel wall on direct immunofluorescence. There is no grenz zone and eosinophils are less in number in erythema elevatum diutinum as against granuloma faciale. Clonal T-lymphocytes may be seen in some cases of pigmented purpuric dermatosis (PPD) and there may be overlap of features between mycosis fungoides and PPD. Cryoglobulinemia shows homogenous eosinophilic periodic acid-Schiff positive deposits in small vessels or ulcer base.

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