EXPORT CITATION

Chapter-22 Ductal Plate Malformation-related Hereditary Liver Diseases

BOOK TITLE: Liver Biopsy Made Easy

Author
1. Gupta Nalini Bansal
ISBN
9789386150264
DOI
10.5005/jp/books/14215_23
Edition
1/e
Publishing Year
2018
Pages
7
Author Affiliations
1. SRL Ltd, Fortis Escorts Heart Institute, New Delhi, India
Chapter keywords
Ductal plate malformation, DPM, Caroli’s syndrome, Caroli’s disease, autosomal dominant polycystic disease, choledochal cyst, liver biopsy, congenital hepatic fibrosis

Abstract

This chapter describes ductal plate malformation-related hereditary liver diseases. Ductal plate malformation (DPM)-related hereditary liver diseases are also called as fibropolycystic diseases of liver. DPM-related hereditary liver diseases include congenital hepatic fibrosis, autosomal recessive polycystic disease, autosomal dominant polycystic disease, Caroli’s disease, and choledochal cysts. This chapter covers the congenital hepatic fibrosis, Caroli’s syndrome, Caroli’s disease, autosomal dominant polycystic disease, choledochal cyst, Von meyenberg complex or biliary microhamartoma, and liver biopsy sign out. CHF are often misdiagnosed as cirrhosis radiologically. Biopsy features of absence of inflammation, single cell plate thick hepatocyte cords, and absent portal vein profiles in most tracts help to differentiate from cirrhosis.

Related Books

© 2019 Jaypee Brothers Medical Publishers (P) LTD.   |   All Rights Reserved