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Chapter-09 Blistering (Vesiculobullous) Diseases

BOOK TITLE: Review of Dermatology

Author
1. Jindal Saurabh
ISBN
9789386322302
DOI
10.5005/jp/books/14213_10
Edition
1/e
Publishing Year
2018
Pages
27
Author Affiliations
1. Mahatma Gandhi Mission Medical College, Navi Mumbai, Maharashtra, India, MGM Medical College and Hospital, Navi Mumbai, Maharashtra, India, Dr Jindal’s Skin and Dental Clinic, Karkardooma, New Delhi; Max Superspeciality Hospital, Vaishali, Ghaziabad, MGM Medical College, Navi Mumbai, Maharashtra India
Chapter keywords
Blistering disease, vesiculobullous disease, blistering disorder, acquired blistering disorder, blister formation, congenital blistering disorder, inherited blistering disorder, Hailey-Hailey disease, Darier’s disease, congenital epidermolysis bullosa, pemphigus, pemphigoid, pemphigoid gestationis, cicatricial pemphigoid, epidermolysis bullosa acquisita, dermatitis herpetiformis

Abstract

This chapter discusses about blistering diseases or vesiculobullous diseases. Blistering disorders are classified based on etiology and level of blister formation. There can be acquired blistering disorders as in an autoimmune mechanism of blister formation and congenital blistering disorders as in genetic defects. Pemphigus, pemphigoid, pemphigoid gestationis, cicatricial pemphigoid, epidermolysis bullosa acquisita, dermatitis herpetiformis, linear IgA bullous dermatosis are discussed under acquired blistering disorders. Inherited blistering disorders cover Hailey-Hailey disease, Darier’s disease, and congenital epidermolysis bullosa. The chapter ends with multiple choice questions with answers that are important from the point of view of examinations and appeared in National Eligibility Cum Entrance Test (NEET), PGI, and All India Institute of Medical Sciences (AIIMS) examinations.

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