Vitamin D-dependent rickets (VDDR) is a disorder of bone development characterized by softened weak bones. It is of two types-vitamin D-dependent rickets-I (VDDR-I) and vitamin D-dependent rickets type II (VDDR-II). Vitamin D-dependent rickets type II is a rare autosomal recessive disorder. The patients exhibit characteristic clinical features as well as numerous dental manifestations such as hypoplastic teeth, missing teeth, enlarged pulp chambers, and recurrent spontaneous abscesses. The case presented in this article is of vitamin D-dependent rickets type II in a pediatric dental patient who reported with multiple missing teeth and required treatment consisting of restorations and extractions. The aim of the present article is to raise awareness on the characteristics of this disorder, as well as its treatment and dental considerations.