Sinus of Valsalva aneurysm is an uncommon disease. Rarely, the aneurysm presents with evidence of obstruction of the right ventricular outflow tract, aortic insufficiency, coronary artery compression, or conduction abnormalities in the absence of rupture. We report a case with an unruptured aneurysm of the right sinus of Valsalva extending into the interventricular septum causing complete heart block, which was managed successfully by surgery. We emphasize the rarity of this pathology and highlighting the importance of multiplane transesophageal echocardiography in its assessment, providing a complete anatomic functional characterization, allowing precise identification of structural anomalies, valve abnormalities, and cardiac function, thereby guiding appropriate surgical management.