Coronary arteriovenous fistula (CAVF) is a rare form of congenital heart disease. Among the CAVFs, the right coronary artery (RCA) fistula is common. The majority of patients remain asymptomatic, and CAVFs are detected incidentally. Coronary angiography remains the primary diagnostic and therapeutic modality in the assessment of the fistula. In the perioperative setting, transesophageal echocardiography (TEE) is the modality of choice, which has been rarely reported to date. It not only confirms the fistulous tract but also confirms the other associated anomalies, biventricular function, and the adequacy of surgical repair.
We report a TEE imaging of CAVF between the left circumflex artery (LCx) and right-sided superior vena cava (SVC).