Anesthetic Management of a Patient with Coffin–Siris Syndrome

JOURNAL TITLE: Journal of Research & Innovation in Anesthesia

Author
1. Pinakin Gujjar
2. Deepa Divakar
3. Pravin Virappa Ubale
ISSN
DOI
10.5005/jp-journals-10049-0061
Volume
4
Issue
1
Publishing Year
2019
Pages
2
Author Affiliations
1. com.mps.common.model.Contributor@50a0685a ,
2. com.mps.common.model.Contributor@48010de8 ,
3. com.mps.common.model.Contributor@25389d7b
Article keywords
Coarse facial features, Coffin–Siris syndrome, Difficult airway

Abstract

Coffin–Siris syndrome (CSS) is a rare genetic condition with characteristic musculoskeletal abnormalities and growth restrictions, coarse facial features, feeding abnormalities, systemic malformation, and developmental and cognitive delay.1–3 Main anesthetic concerns should be difficult airway that tends to get worse with age, risk of aspiration, and periop pulmonary complications in uncooperative and mentally retarded patients. We report a case of 9-years-old male patient with CSS for dental extraction and restoration under general anesthesia.

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