Alpha-2-macroglobulin-like-1 protein (A2ML1) 51, 54, 55

A2ML1 see Alpha-2-macroglobulin-like-1 protein (A2ML1)

Anchoring fibrils 81, 87

Annular erythema 39

Antiendothelial antibodies 155

Antineutrophil cytoplasmic antibodies (ANCA) 155

Antinuclear antibodies (ANAs) 39, 40, 45, 119

Anti-p200 pemphigoid 84, 107–109

Atrophie blanche see Livedoid vasculopathy (LV)

Basement membrane zone (BMZ) 45, 53, 54, 65, 66, 66, 68, 69, 69, 72, 75, 76, 78, 81, 83, 87, 88, 90, 90, 91, 93, 94, 95, 97, 98, 98, 99, 102, 103, 104, 119, 120, 122, 123, 134, 135, 135, 136, 136, 137, 142, 144, 168

BLE see Bullous lupus erythematosus (BLE)

BMZ see Basement membrane zone (BMZ)

BP see Bullous pemphigoid (BP)

BP180 65, 70, 75, 78, 93, 94, 97, 98, 101, 103, 108

BP230 65, 70, 75, 78, 87, 93, 101, 103

BPAg1 see BP230

BPAg2 see BP180

Brunsting–Perry variant see Mucous membrane pemphigoid

Bullosis diabeticorum 177

Bullous impetigo, 17

Bullous lupus erythematosus (BLE) 68, 84, 87–91, 93

Bullous pemphigoid (BP) 7, 10, 15, 51, 65–72, 75, 82, 89, 93, 101, 133

Castleman disease 51

Caterpillar bodies 167, 169

CBDC see Chronic bullous dermatosis of childhood (CBDC)

Celiac disease 113

Chronic bullous dermatosis of childhood (CBDC) 93

Chronic ulcerative stomatitis (CUS) 45–48

Cicatricial pemphigoid see Mucous membrane pemphigoid (MMP)

Cirrhosis 161

Civatte bodies 134, 134–136, 136, 137, 141

Colloid bodies 101, 102, 102, 104, 134, 134–136, 136, 137, 141

Connective tissue diseases 39–43, 46, 113, 119

Corticosteroids 45, 68, 133, 155

CREST syndrome 39

Crohn disease 81

CUS see Chronic ulcerative stomatitis (CUS)

CUS protein (CUSP) 45

Cytoid bodies 45, 53, 54, 55, 119, 121, 123, 124, 128, 129, 141–142 142–145

DEJ see Dermoepidermal junction (DEJ)

Deoxyribonucleic acid (DNA) 39, 123, 127

Dermatitis herpetiformis (DH) 113–117

Dermatomyositis 39 see also Connective tissue diseases

Dermoepidermal junction (DEJ) 40, 54, 57–58, 60, 61, 89, 97, 98, 101, 102, 103, 107, 109, 115, 116, 117, 120, 121, 127, 128, 128, 129, 129, 134, 145, 167, 168, 170, 171, 173, 175

Desmocollin 9, 21, 25, 27, 31, 34

Desmoglein 1 (Dsg1) 3, 9, 15, 21, 31, 34, 51, 57, 58

Desmoglein 3 (Dsg 3) 3, 9, 15, 21, 31, 34, 51, 59

Desmoplakin 51

Desmosomal plaque 3, 9, 15, 57

Desmosome 51

Desquamative gingivitis 75, 101

Discoid lupus erythematosus (DLE) 119 see also Lupus erythematosus (LE)

DLE see Discoid lupus erythematosus (DLE)

DNA see Deoxyribonucleic acid (DNA)

EBA see Epidermolysis bullosa acquisita (EBA)

Eccrine coil 180, 181

EM see Erythema multiforme (EM)

Envoplakin 51, 54, 55

Eosinophilic spongiosis 3, 15, 21, 66

Epidermal transglutaminase (eTG) 113

Epidermolysis bullosa acquisita (EBA) 65, 77, 81–84, 89, 93

Epiligrin 75, 78

Epitope spreading 3, 15, 31, 51, 57, 59, 87, 101

Erythema multiforme (EM) 52, 93, 127, 129, 141

Extractable nuclear antigens (ENAs) 39, 41, 42, 43

FDE see Fixed drug eruption (FDE)

Festooning 167, 168, 169, 173, 174

Fibrinoid necrosis 156

Finkelstein's disease 155 see also Hemorrhagic edema of infancy

Fixed drug eruption (FDE) 141

Fogo selvagem (FS) 15

FS see Fogo selvagem (FS)

Gammopathy 25, 31, 51

Gluten-sensitive enteropathy (GSE) 113

GSE see Gluten-sensitive enteropathy (GSE)

Halogenoderma 9

Hemidesmosome 51, 65

Hemorrhagic edema of infancy 155

Henoch–Schönlein purpura (HSP) 150–151, 155–158

Hepatitis C 133, 167

Herpes gestationis see Pemphigoid gestationis (PG)

Histone 39

HSP see Henoch-Schönlein purpura (HSP)

Human leukocyte antigen (HLA) 3, 15, 75, 81, 97, 113, 133, 155

Hydroxycloroquine 45

Hypersensitivity vasculitis see Leukocytoclastic vasculitis (LCV)

IEN see Intraepidermal neutrophilic (IEN) variant

IgA paraneoplastic pemphigus 25

IgA pemphigus see Immunoglobulin A (IgA) pemphigus

IgA vasculitis 155

IgG4 15, 18, 21, 65, 66, 75, 108

IgG/IgA pemphigus 31–34

Immunoglobulin A (IgA) pemphigus 25–26

Inflammatory bowel disease 9, 31, 81

Integrin 75, 78

Interface dermatitis/mucositis 141–145

Interface tissue reaction 141

Intraepidermal neutrophilic (IEN) variant 25, 27, 28

La (SSB) 42, 43

LABD see Linear IgA bullous dermatosis (LABD)

Lamina densa 65, 67, 71, 87, 89

Lamina lucida 65–67, 71, 89, 93

Laminin 332 (laminin 5) 75, 78

Laminin γ-1 107, 109

LCV see Leukocytoclastic vasculitis (LCV)

LE see Lupus erythematosus (LE)

Leukocytoclasis 149, 150, 156

Leukocytoclastic vasculitis (LCV) 149–152

Lichen planopilaris 133

Lichen planus (LP) 45, 52, 65, 101, 133–137

Lichen planus pemphigoides (LPP) 101–104

Linear IgA bullous dermatosis (LABD) 93–95

Livedoid vasculopathy (LV) 177, 179

LP see Lichen planus (LP)

LPP see Lichen planus pemphigoides (LPP)

Lupus band 57, 58, 60, 88, 122, 123, 128, 136

Lupus band test (LBT) 120–123, 127

Lupus erythematosus (LE) 39, 57, 58, 60, 119–124, 127, 128, 136, 150, 178 see also Connective tissue diseases

Lymphoma 25, 51, 113

Max-Joseph space 101

Milia 75, 81, 107, 167, 173

Mixed connective tissue disease 39

Monkey esophagus 5, 9, 18, 21, 26, 33, 59, 69, 116

Mucous membrane pemphigoid (MMP) 45, 65, 75–78, 82–84, 93, 108

Myeloma 25

NC16A 65, 70, 98, 101, 103

Neutrophilic karyorrhexis 87, 89

Neutrophilic spongiosis 21, 25, 26

Nikolsky sign 3, 15, 57

Nonbullous neutrophilic lupus erythematosus 87–88

n-serrated pattern 68, 77, 78, 82, 95, 107, 109

Paraneoplastic autoimmune multiorgan syndrome (PAMS) 51 see also Paraneoplastic pemphigus (PNP)

Paraneoplastic pemphigus (PNP) 51–55, 101

PCT see Porphyria cutanea tarda (PCT)

PE see Pemphigus erythematosus (PE)

Pemphigoid gestationis (PG) 97–99

Pemphigus erythematosus (PE) 57–61

Pemphigus foliaceus (PF) 3, 15–18, 21, 31, 57

Pemphigus herpetiformis (PH) 21–23, 31

Pemphigus vegetans 9–13

Pemphigus vulgaris (PV) 3–8, 15, 21, 25, 31

Penicillamin 57, 65, 87

Periplakin 51, 54, 55

PF see Pemphigus foliaceus (PF)

PG see Pemphigoid gestationis (PG)

Pigmented purpuric dermatoses (PPD) 161, 163

Plectin 51

PNP see Paraneoplastic pemphigus (PNP)

Porphyria cutanea tarda (PCT) 167–171, 173

Porphyrin 169, 173

Pruritic urticarial papules and plaques of pregnancy (PUPPP) 97

Pseudoporphyria 173–175

PUVA-induced blisters 127, 128

PV see Pemphigus vulgaris (PV)

Pyodermatitis-pyostomatitis vegetans 9

Rat bladder 54, 103

Ribonucleoprotein (RNP) 41

Ro (SSA) 41, 42, 43

‘Row of tombstones’ 3, 5

Salt-split skin (SSS) 67, 71, 76, 89, 93, 98, 108

Sandwich double antibody immunofluorescence method 66

Scarring 65, 75, 77, 81, 82, 107, 113, 119, 120, 133, 167, 173

Scl-70 41, 42, 43

Scleroderma 39, 41 see also Systemic sclerosis

Senear–Usher syndrome see Pemphigus erythematosus (PE)

Seroreversion 55

Sjögren syndrome 39 see also Connective tissue diseases

Sm antigen 41

Solar elastosis 127, 128

SPD variant see Subcorneal pustular dermatosis (SPD) variant

Stasis dermatitis 177

Stevens–Johnson syndrome (SJS)/toxic epidermal necrolysis (TEN) 141

‘String of beads’ 93

Subacute cutaneous lupus erythematosus (SCLE) 119 see also Lupus erythematosus (LE)

Subcorneal pustular dermatosis (SPD) variant 25, 26, 28

Sweat gland 128, 178

Systemic lupus erythematosus (SLE) 87, 119

Systemic sclerosis 39, 41 see also Connective tissue diseases

Tissue transglutaminase (tTG) 113

Type IV collagen 68, 71, 87

Type VII collagen 75, 78, 81, 84, 87, 89, 90, 93, 108, 109, 123

Tzanck smear 3

Ulcerative colitis 11, 81

Ultraviolet light 57, 127, 167, 173

Uroporphyrinogen decarboxylase 167, 169

Urticarial vasculitis 149

u-serrated pattern 77, 82, 83, 83

Vacuolar interface dermatitis 39, 40, 57, 141, 142, 144

Vancomycin 93

Waldenstrom macroglobulinemia 51

Wickham's striae 101, 133