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Atlas of Hematology
Renu Saxena, HP Pati, M Mahapatra
CHAPTER 1:
Anemias
INVESTIGATION
HYPOCHROMIC MICROCYTIC ANEMIA
Iron Deficiency Anemia
Causes of Iron Deficiency
Clinical Features
Treatment
Parenteral Iron
Grading Iron Stains in Bone Marrow Aspirates (Table 1.1)
SIDEROBLASTIC ANEMIA
Classification of Sideroblastic Anemia
Hereditary
Acquired
Drugs
Rare Causes
MACROCYTIC ANEMIA
B12 Deficiency
Management of B12 Deficiency
Folic Acid Deficiency
Management
DIMORPHIC ANEMIA
MYELODYSPLASTIC SYNDROME (MDS)
Morphology
NORMOCYTIC NORMOCHROMIC ANEMIA
CHAPTER 2:
Bone Marrow Failure Syndromes
APLASTIC ANEMIA
Aplastic Anemia with Patchy Cellularity
Criteria for Aplastic Anemia
Severity of Aplastic Anemia (AA)
Clinical Features
DIFFERENTIAL DIAGNOSIS OF PANCYTOPENIA
Pancytopenia with Hypocellular Bone Marrow
Pancytopenia with Cellular Bone Marrow
Complications
Treatment
FANCONI'S ANEMIA
Treatment
Outcome
PAROXYSMAL NOCTURNAL HEMOGLOBINURIA (PNH)
PURE RED CELL APLASIA (PRCA)
CHAPTER 3:
Hemolytic Anemias
PERIPHERAL BLOOD EXAMINATION
DIAGNOSIS OF HEMOGLOBINOPATHIES
COMMON HIGH PERFORMANCE LIQUID CHROMATOGRAPHY (HPLC) PATTERNS (FIGS 3.10 TO 3.23)
CONGENITAL DYSERYTHROPOIETIC ANEMIA (CDA)
Clinical Features
Other Clinical Features
Treatment
THALASSEMIA
β-Thalassemia Trait
β-Thalassemia Intermedia
β-Thalassemia Major (Cooley's anemia)
Management
HEREDITARY SPHEROCYTOSIS
Clinical Features
CHAPTER 4:
Disorders of Platelets
THROMBOCYTOPENIA
Causes of Thrombocytopenia
Decreased Bone Marrow Production of Platelets
Increased Destruction of Platelets
Platelet Sequestration
Dilutional Loss of Platelets
Hereditary Thrombocytopenia
PRIMARY IMMUNE THROMBOCYTOPENIA (ITP)
Clinical Features
Treatment of ITP
THROMBOTIC THROMBOCYTOPENIC PURPURA/HUS
PLATELET FUNCTION DEFECTS
Clinical features
THROMBOCYTOSIS
Treatment
CHAPTER 5:
Acute Leukemia
ACUTE LEUKEMIA
ALL vs AML
ACUTE LYMPHOBLASTIC LEUKEMIA (ALL)
Clinical Features
BLAST MORPHOLOGY
L1 Blasts (Fig. 5.2)
L2 Blasts (Fig. 5.3)
L3 Blasts (Fig. 5.4)
Diagnosis
Blood and Peripheral Smear
Bone Marrow
Large Granular Lymphocytic Leukemia
Morphology of Large Granular Lymphocytes (Fig. 5.6)
Treatment for ALL
Prognosis
Criteria for Complete Response to Therapy in Acute Leukemia
ACUTE MYELOID LEUKEMIA (AML)
WHO Categorization of AML
Diagnosis
Blood and Peripheral Smear
Bone Marrow
Cytochemistry
Immunophenotyping in Acute Leukemia
Electron Microscopy
BIPHENOTYPIC LEUKEMIA
Biphenotypic or Mixed Lineage Acute Leukemias
AML WITH MULTILINEAGE DYSPLASIA
ACUTE MYELOBLASTIC LEUKEMIA/MYELODYSPLASTIC SYNDROME: OCCUPATION RELATED OR THERAPY RELATED
Criteria for Complete Response to Therapy in Acute Leukemia
Clinical Features
Prognostic Factors
Treatment
Prognosis
CHAPTER 6:
Chronic Leukemia
CHRONIC MYELOID LEUKEMIA (CML)
Diagnosis
Phases of Chronic Myeloid Leukemia
Note
Clinical Symptoms and Signs
Treatment
POLYCYTHEMIA VERA (FIGS 6.6 AND 6.7)
Major Criteria
Minor Criteria
ESSENTIAL THROMBOCYTHEMIA (FIGS 6.8 AND 6.9)
CHRONIC LYMPHOCYTIC LEUKEMIA (CLL) (FIGS 6.10 TO 6.12)
Diagnosis
Differential Diagnosis
Clinical Features and Presentation
Treatment
Prognosis
PROLYMPHOCYTIC LEUKEMIA (PLL) (FIG. 6.13)
HAIRY CELL LEUKEMIA (HCL) (FIGS 6.14 TO 6.17)
CHAPTER 7:
Myelofibrosis
CHAPTER 8:
Plasma Cell Dyscrasias
MONOCLONAL GAMMOPATHY OF UNDETERMINED SIGNIFICANCE (MGUS)
SMOLDERING MYELOMA
MULTIPLE MYELOMA
Note
Features of MGUS
SOLITARY PLASMACYTOMA OF THE BONE
AMYLOIDOSIS
Clinical Features and Presentation
Investigations in a Case of Suspected Myeloma
Treatment
Prognosis
CHAPTER 9:
Infections
SEPTICEMIA
HEMOPHAGOCYTOSIS
Storage Disorders
MALARIA
MICROFILARIA
TUBERCULOSIS
CHAPTER 10:
Stem Cell Transplant
CAUSES OF MARROW TRANSPLANTATION FAILURE
POST-TRANSPLANT MDS
INDEX
TOC
Index
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