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Textbook of Pediatric Dermatology
Arun C Inamadar, Aparna Palit, S Ragunatha
CHAPTER 1:
Structure and Functions of the Skin
EMBRYOGENESIS OF THE SKIN
EMBRYONIC SKIN
Embryonic-Fetal Transition
Second Trimester
Third Trimester
UNIQUE FEATURES OF DEVELOPING SKIN
Periderm
Regionalization in Developing Skin
Keratinization
Appendage Formation
Nail Formation
Eccrine Gland Formation
Pilosebaceous Apparatus
Applied Importance
STRUCTURE OF THE NEWBORN SKIN
Epidermis
Basal Layer
Spinous Layer
Granular Layer
Horny Layer
Non-keratinocytes
Appendages
Dermoepidermal Junction
Dermis
Blood Vessels and Lymphatics
FUNCTIONS OF THE NEWBORN SKIN
Mechanical Functions
Physical Functions
Chemical Functions
Maintenance of Homeostasis
Ultraviolet Protection
Synthesis of Essential Nutrients and Endocrinal Functions
Immunological Functions
SKIN OF THE PREMATURE INFANT
SKIN CARE
Skin Care at Birth
Removal of Vernix Caseosa
Washing and B athing
Neonatal Skin Care
Skin Care of the Diaper Area and Napkin Changes
Infant Wipes
Scalp
Nails
Ears
Umbilicus
Skin Care in the Premature Infant
Preventive Measures
Skin Care of the Term Baby and Infant
Role of Cosmetic Products
Role of Massage
CHAPTER 2:
Neonatal Dermatology
INTRODUCTION
TRANSIENT NEONATAL DERMATOSIS
Vernix Caseosa
Physiological Desquamation
Sebaceous Gland Hyperplasia
Milia
Epstein Pearls
Erythema Toxicum Neonatorum (Toxic Erythema of Newborn)
Transient Neonatal Pustular Melanosis (Neonatal Pustular Melanosis, Lentigines Neonatorum)
Miliaria
Color Changes in Neonate
Color Changes due to Vascular Anomalies
Color Changes due to Pigmentary Anomalies
Pigmentary Changes Caused by Bilirubin, Meconium or Vernix
Suction Blister
Sucking Pads/Calluses
Lanugo Hair
Miniature Puberty
Acne Neonatorum
DEVELOPMENTAL ABNORMALITIES
Cysts
Thyroglossal Duct Cysts
Bronchogenic Cysts
Dermoid Cysts
Branchial Clefts and Sinuses
Aplasia Cutis Congenita and Scalp Defects
Amniotic Band Syndrome
Dimples
Benign Neoplasm
Miscellaneous
Encephalocele
Congenital Lip Pits
CUTANEOUS SIGNS OF SPINAL DYSRAPHISM
Skin Dimples
Tuft of Hair
Myelocele
Aplasia Cutis
Sacral Hemangioma
Human Tail
CUTANEOUS MANIFESTATIONS OF CONGENITAL INFECTIONS
Etiology
Candidiasis
TORCH Infections
Toxoplasmosis
Rubella
Cytomegalovirus Infection
Herpes Simplex Virus Infection
Varicella Zoster Virus Infection
Fetal Varicella Syndrome
Neonatal Varicella
Human Immunodeficiency Virus Infection
Congenital Syphilis
CHAPTER 3:
Genodermatosis
INTRODUCTION
PRINCIPLES OF GENETICS
MAJOR PATTERNS OF GENETIC TRANSMISSION
Mitochondrial Inheritance
Sporadic Disorder
Penetrance and Expressivity
Heterogeneity
Clinical Heterogeneity
Genetic Heterogeneity
Locus Heterogeneity/Nonallelic Heterogeneity
Allelic Heterogeneity
Contiguous Gene Syndromes
Cutaneous Mosaicism
Chromosomal Disorders
GENETIC COUNSELING
PRENATAL DIAGNOSIS OF HEREDITARY SKIN DISORDERS
CLASSIFICATION OF GENODERMATOSES
ECTODERMAL DYSPLASIA
X-Linked Hypohidrotic/Anhidrotic Ectodermal Dysplasia (Christ-Siemens-Touraine Syndrome)
Genetics
Clinical Features
Diagnosis
Differential Diagnosis
Management
Hidrotic Ectodermal Dysplasia (Clouston's Syndrome)
Genetics
Clinical Features
Diagnosis
Management
Ectrodactyly-Ectodermal Dysplasia-Cleft Lip/Palate Syndrome
Genetics
Clinical Features
Diagnosis
Differential Diagnosis
Management
Rapp-Hodgkin Syndrome/Hay-Wells Syndrome (AEC Syndrome)
Dyskeratosis Congenita (Zinsser-Cole-Engman Syndrome)
Incontinentia Pigmenti (Bloch-Sulzberger Disease)
Genetics
Clinical Features
Investigations
Diagnosis
Differential Diagnosis
Management
Oral-Facial-Digital Syndrome
Johanson-Blizzard Syndrome
Schöpf-Schulz-Passarge Syndrome
HEREDITARY DISORDERS OF PIGMENTATION
Disorders with Hypopigmentation
Piebaldism
Waardenburg Syndrome
Oculocutaneous Albinism
Hermansky-Pudlak Syndrome
Disorders with Hyperpigmentation
LEOPARD Syndrome
Carney Complex
HEREDITARY DISORDERS OF IMMUNE SYSTEM
Ataxia Telangiectasia
Chronic Mucocutaneous Candidiasis
Chédiac-Higashi Syndrome
Complement Deficiency Disorders
C 2 Deficiency
Leiner's Disease
Other Complement Deficiency Disorder
Chronic Granulomatous Disease of Childhood
DiGeorge Syndrome
Hyperimmunoglobulin E Syndrome
Immunoglobulin Deficiency
Selective IgA Deficiency
Selective IgM Deficiency
X-linked Hypogammaglobulinemia
Pan-hypogammaglobulinemia
Severe Combined Immunodeficiency
Wiskott-Aldrich Syndrome
Anhidrotic Ectodermal Dysplasia with Immunodeficiency
Genetics
Clinical Features
Diagnosis
Treatment
HEREDITARY DISORDERS WITH PHOTOSENSITIVITY
Porphyrias
Classification
Congenital Erythropoietic Porphyria
Erythropoietic Protoporphyria
Erythropoietic Coproporphyria
Porphyria Cutanea Tarda
Hepatoerythropoietic Porphyria
Acute Intermittent Porphyria
Variegate Porphyria
Chester Porphyria
Hereditary Coproporphyria
Investigations in Porphyrias
Differential Diagnosis of Porphyria
Management of Porphyrias
Inherited DNA-Repair Disorders and Chromosome Instability Syndromes
Bloom Syndrome (Congenital Telangiectatic Erythema and Stunted Growth)
Xeroderma Pigmentosum
De Sanctis-Cacchione Syndrome
XP-variant
Pigmented Xerodermoid
Cockayne Syndrome
Trichothiodystrophy
Rothmund-Thomson Syndrome (Poikiloderma Congenitale)
Kindler's Syndrome
HEREDITARY DISORDERS OF METABOLISM
Disorders of Amino Acid Metabolism
Phenylketonuria
Homocystinuria
Tyrosinemia II (Richner Hanhart Syndrome)
Alkaptonuria (Ochronosis)
Hartnup Disease
MULTIPLE TUMOR SYNDROMES
Neurofibromatosis
Neurofibromatosis I (von-Recklinghausen's Disease)
Segmental NF-1
Neurofibromatosis II (Bilateral Acoustic Schwannoma)
Tuberous Sclerosis Complex (Bourneville's Disease, Epiloia)
Genetics
Pathogenesis
Clinical Features
Associations
Diagnosis
Differential Diagnosis
Management
Gardner Syndrome
Genetics
Clinical Features
Cowden Syndrome (Multiple Hamartoma Syndrome)
HEREDITARY DISORDERS OF CONNECTIVE TISSUE
Pseudoxanthoma Elasticum (Grönblad-Strandberg Syndrome)
Pathogenesis
Clinical Features
Diagnosis
Management
Cutis Laxa (Generalized Elastolysis)
Pathogenesis
Clinical Features
Diagnosis
Management
Acquired Cutis Laxa
Marfan Syndrome
Pathogenesis
Clinical Features
Diagnosis
Management
Buschke-Ollendorff Syndrome (Dermatofibrosis Lenticularis Disseminata)
Clinical Features
Diagnosis
Management
Ehlers-Danlos Syndrome (Cutis Hyperelastica)
Classification
Clinical Features
Diagnosis
Management
Osteogenesis Imperfecta
Pathogenesis
Clinical Features
Diagnosis
Management
Differential Diagnosis
Lipoid Proteinosis
PREMATURE AGING SYNDROMES
True Premature Aging
Hutchinson-Gilford Syndrome (Progeria)
Werner Syndrome
Cockayne Syndrome
Rothmund Thomson Syndrome
Conditions with Skin Atrophy/Lipoatrophy
Wiedemann-Rautenstrauch Syndrome (Neonatal Progeroid Syndrome)
De Barsy Syndrome
Acrometageria
Conditions with Skin Laxity
Cutis Laxa
Wrinkly Skin Syndrome
Conditions with Aged Appearance of the Individual
CHROMOSOMAL DISORDERS
Autosomal Disorders
Down's Syndrome (Mongolism)
Sex-Chromosomal Disorder
Turner Syndrome (Gonadal Dysgenesis)
Klinefelter's Syndrome
SKIN GENE THERAPY
Goals of Skin Gene Therapy
Target Cells for Skin Gene Therapy
Epidermal Keratinocytes
Epidermal Stem Cells
Fibroblasts
Approaches to Skin Gene Therapy
Techniques to Insert the Gene into the Cells
Candidate Diseases for Skin Gene Therapy
Limitations of Skin Gene Therapy
CHAPTER 4:
Inherited Ichthyosis and other Hereditary Disorders of Keratinization
INHERITED ICHTHYOSIS
Introduction
Classification
Ichthyosis Vulgaris
X-linked Recessive Ichthyosis
Harlequin Ichthyosis
Lamellar Ichthyosis
Nonbullous Ichthyosiform Erythroderma (Congenital Ichthyosiform Erythroderma)
Collodion Baby
Bathing-Suit Ichthyosis
Epidermolytic Hyperkeratosis or Bullous Congenital Ichthyosiform Erythroderma
Superficial Epidermolytic Ichthyosis or Ichthyosis Bullosa of Siemens
Annular Type of Epidermolytic Ichthyosis
Ichthyosis Hystrix
Multiple Sulfatase Deficiency
Complications
Diagnostic Approach to Inherited Ichthyosis
Investigations
Differential Diagnosis
Management
ICHTHYOSIFORM SYNDROMES
Sjögren-Larsson Syndrome
Refsum Disease (Hereditary Motor and Sensory Neuropathy Type 4)
MEDNIK Syndrome
Ichthyosis Follicularis, Alopecia and Photophobia Syndrome
Conradi-Hünermann-Happle Syndrome
Neutral Lipid Storage Disease with Ichthyosis (Chanarin-Dorfman Syndrome)
KID Syndrome
CHILD Syndrome
Netherton Syndrome
Trichothiodystrophy
ERYTHROKERATODERMA
Erythrokeratoderma Variabilis (Mendes da Costa Syndrome)
Progressive Symmetric Erythrokeratoderma of Darier-Gottron (Gottron's Syndrome)
Erythrokeratoderma En Cocardes of Degos (Dego's Syndrome)
Peeling Skin Syndrome
PALMOPLANTAR KERATODERMA
Diffuse Palmoplantar Keratoderma
Vörner's Keratoderma
Thost-Unna Keratoderma
Greither's Syndrome
Vohwinkel's Syndrome (Cicatrizing Keratoderma with Hearing Impairment)
Camisa's Syndrome (Loricrin Keratoderma or Variant Vohwinkel's Syndrome)
Mal de Meleda (Keratoderma Palmoplantaris Transgradiens)
Keratoderma with Scleroatrophy (Huriez Syndrome)
Olmsted Syndrome
Papillon-Lefevre or Haim-Munk Syndrome
Focal Palmoplantar Keratoderma
Watchers Keratoderma (PPK varians)
Striate Keratoderma
Punctate Keratoderma
Marginal Papular Keratoderma (Acrokeratoelastoidosis of Costa)
Focal Keratoderma with Oral Leukokeratosis
Palmoplantar Keratoderma in Association with Other Disorders
Complications of PPK
Diagnosis of PPK
Management of PPK
CHAPTER 5:
Atopic Dermatitis
INTRODUCTION
ETIOPATHOGENESIS
Hereditary Factors
Environmental Factors
Immune Dysregulation
Infectious Agents
Psychological Factors
PREVALENCE AND INCIDENCE OF ATOPIC DERMATITIS
CLINICAL FEATURES
THE KEY STEPS TO DIAGNOSE ATOPIC DERMATITIS
History
Clinical Presentations
Diagnostic Criteria
Laboratory Investigation
Differential Diagnosis
COMPLICATIONS
NATURAL HISTORY AND PROGNOSIS
MANAGEMENT OF ATOPIC DERMATITIS
General Measures
Specific Measures
First Line of Therapy
Topical Therapy
Systemic Therapy
CURRENT INVESTIGATIONAL THERAPIES OF UNPROVEN EFFICACY
Specific Antibodies and Vaccines
Antistaphylococcal Toxin Strategies
Synthetic Antimicrobial Compounds
Anti-inflammatory Therapies and Immunomodulators
Chemokine Antagonists
Interleukin-4 and Interleukin-13 Antagonists
Suplatast Tosilate
Peroxisome Proliferator–Activated Receptor Agonists
Intravenous Immunoglobulin
Omalizumab
Vitamin D and Heliotherapy
Mycobacterium vaccae Vaccine
Antipruritic Therapy with Opioid Receptor Antagonist
Counseling and Psychotherapy
CHAPTER 6:
Eczemas other than Atopic Dermatitis
INTRODUCTION
CLASSIFICATION
Exogenous Eczemas
Endogenous Eczemas
EXOGENOUS ECZEMAS
DiaperDermatitis
Clinical Features
Diagnosis and Differential Diagnosis
Management
Contact Dermatitis
Allergic Contact Dermatitis
Irritant Contact Dermatitis
Phytodermatoses
Irritant Reactions
Hypersensitivity Reactions
Allergic Contact Dermatitis due to Plants
Phytophotodermatitis
ENDOGENOUS ECZEMAS
Autosensitization Dermatitis
Clinical Features
Management
Seborrheic Dermatitis
Clinical Features
Diagnosis and Differential Diagnosis
Management
Perioral Dermatitis
Clinical Features
Diagnosis and Differential Diagnosis
Management
Asteatotic Eczema
Clinical Features
Diagnosis
Management
Nummular Eczema
Clinical Features
Differential Diagnosis
Management
Infectious Eczematoid Dermatitis
Clinical Features
Differential Diagnosis
Treatment
Pityriasis Alba
Clinical Features
Diagnosis and Differential Diagnosis
Management
Pompholyx
Clinical Features
Diagnosis and Differential Diagnosis
Management
Lichen Simplex Chronicus
Clinical Features
Diagnosis and Differential Diagnosis
Management
Prurigo
Prurigo Simplex
Atopic Prurigo
Actinic Prurigo
Prurigo Nodularis
Sutton's Summer Prurigo
Prurigo Pigmentosa
Juvenile Plantar Dermatosis
Clinical Features
Diagnosis and Differential Diagnosis
Management
CHAPTER 7:
Bacterial Infections
INTRODUCTION
CLASSIFICATION
SUPERFICIAL PYOGENIC INFECTIONS
Impetigo
Types
Course
Diagnosis
Treatment
Periporitis Staphylogenes
Folliculitis
Blistering Distal Dactylitis
Acute Paronychia
DEEP PYOGENIC INFECTIONS
Furuncles and Carbuncles
Ecthyma
Ecthyma Gangrenosum and Other Pseudomonal Infections
Cellulitis
Buccal Cellulitis (Blue Cellulitis)
Periorbital and Orbital Cellulitis
Perianal Cellulitis
Erysipelas
Necrotizing Fasciitis
NONPYOGENIC BACTERIAL INFECTIONS
Erythrasma
Trichobacteriosis Axillaris
Pitted Keratolysis
Perianal Streptococcal Dermatitis
Streptococcal Intertrigo
BACTERIAL TOXIN-MEDIATED ILLNESSES
Staphylococcal Scalded Skin Syndrome
Pathogenesis
Clinical Features
Diagnosis
Differential Diagnosis
Management
Meningococcemia
Pathogenesis
Clinical Features
Diagnosis
Differential Diagnosis
Management
Recurrent Toxin-Mediated Perineal Erythema
SECONDARY PYODERMA
SPECIAL SITUATIONS
Recurrent Pyoderma
Skin Infections Caused by MRSA
Emerging Bacterial Infections
Rickettsial Fever
CHAPTER 8:
Cutaneous Mycobacterial Infections
INTRODUCTION
OVERVIEW
CLASSIFICATION AND CLINICAL FEATURES
Primary Cutaneous Tuberculosis in the Nonsensitized or Without Previous Exposure
Miliary Tuberculosis of the Skin
Tuberculous Chancre
Secondary Cutaneous Tuberculosis in Sensitized/Those Exposed to Tuberculous Infection
Lupus Vulgaris
Scrofuloderma
Tuberculosis Verrucosa Cutis
Unusual Presentations
Tuberculids
Lichen Scrofulosorum
Papulonecrotic Tuberculid
Erythema Nodosum
Erythema Induratum
DERMATOLOGICAL COMPLICATIONS DUE TO BCG VACCINATION
INVESTIGATIONS
DIAGNOSTIC APPROACH
TREATMENT
BIBLIOGRAPHY
INTRODUCTION
HISTORY
GENERAL CHARACTERISTICS AND CLASSIFICATION
EPIDEMIOLOGY
PATHOGENESIS
CLINICAL FEATURES
HISTOPATHOLOGY
DIAGNOSIS
DIFFERENTIAL DIAGNOSIS
TREATMENT
COMPLICATIONS, COURSE AND PROGNOSIS
BIBLIOGRAPHY
INTRODUCTION
SUSCEPTIBILITY TO THE DISEASE
RESERVOIR OF INFECTION
PATHOGENESIS OF LEPROSY
Human Leukocyte Antigen Susceptibility
Antigen Presentation
Induction of Immune Response
Expression of Immune Response
CLASSIFICATION OF LEPROSY
WHO Classification of Leprosy for Therapy
WHO Clinical Classification for Therapy by Field Workers
LEPROSY IN CHILDREN
Prevalence
Clinical Features
DIAGNOSIS OF LEPROSY
TREATMENT OF LEPROSY
Mode of Action
WHO Multidrug Therapy Regimens
For Multibacillary Leprosy
For Paucibacillary Leprosy
For Children under 10 Years of Age
REACTIONS IN LEPROSY
Treatment of Reactions
Management of Type 1 Reaction
Management of Type 2 Reaction
LEPROSY-RELATED DEFORMITIES IN CHILDREN
SUMMARY
CHAPTER 9:
Viral Infections and Exanthem
INTRODUCTION
HERPESVIRUSES
Herpes Simplex Virus
Epidemiology and Transmission
Clinical Features
Complications
Diagnosis
Treatment
Prognosis
Salient Features
Varicella-Zoster Virus Infections
Varicella
Herpes Zoster
Epstein-Barr Virus Infections
Cytomegalovirus Infections
Epidemiology
Clinical Features
Diagnosis
Treatment
Prognosis
Salient Features
POXVIRUSES
Molluscum Contagiosum
Epidemiology and Transmission
Pathogenesis
Clinical Features
Diagnosis
Treatment
Prognosis
Salient Features
Orf
Epidemiology
Clinical Features
Diagnosis
Treatment
Milker's Nodule
Epidemiology
Clinical Features
Treatment
HUMAN PAPILLOMAVIRUSES
Epidemiology and Transmission
Pathogenesis
Clinical Features
Common Warts
Plantar Warts
Flat Warts
Filiform Warts
Anogenital Warts
Diagnosis
Differential Diagnosis
Treatment
Topical Therapy
Ablative Therapies
Systemic Treatment
Treatment of Genital Warts
HPV Vaccine
Prognosis
Salient Features
EPIDERMODYSPLASIA VERRUCIFORMIS
Epidemiology
Clinical Features
Diagnosis
Treatment
Salient Features
HECK'S DISEASE
VIRAL HEMORRHAGIC FEVERS
Chikungunya Fever
Epidemiology
Transmission
Clinical Features
Diagnosis
Treatment
Prevention
Salient Features
Dengue Fever
Epidemiology
Transmission
Clinical Features
Diagnosis
Treatment
Prevention
Salient Features
BIBLIOGRAPHY
INTRODUCTION
TRADITIONAL EXANTHEMS
Erythema Infectiosum
Historical Aspects
Etiology
Epidemiology
Pathogenesis
Clinical Features
Complications, Course and Prognosis
Treatment
Salient Features
Hand-Foot-Mouth Disease
Historical Aspects
Etiology
Epidemiology
Pathogenesis
Clinical Features
Diagnosis
Course and Prognosis
Complications
Treatment
Salient Features
Infectious Mononucleosis
Historical Aspects
Etiology
Epidemiology
Pathogenesis
Clinical Features
Systemic Complications
Investigation and Diagnosis
Course and Prognosis
Treatment
Salient Features
Measles
Historical Aspects
Etiology
Epidemiology
Clinical Features
Diagnosis
Complications
Treatment
Salient Features
Roseola Infantum
Historical Aspects
Epidemiology
Etiology
Pathogenesis
Clinical Features
Complications
Diagnosis
Treatment
Salient Features
Rubella
Historical Aspects
Etiology
Epidemiology
Clinical Features
Complications
Diagnosis
Treatment
Salient Features
NEWLY REDISCOVERED VIRAL EXANTHEMS
Asymmetric Periflexural Exanthem
Historical Aspects
Etiology
Epidemiology
Clinical Features
Differential Diagnosis
Course and Prognosis
Treatment
Salient Features
Acute Hemorrhagic Edema of Infancy
Historical Aspects
Definition
Etiology
Epidemiology
Pathogenesis
Clinical Features
Investigations
Course and Prognosis
Treatment
Salient Features
Eruptive Pseudoangiomatosis
Historical Aspects
Etiology
Epidemiology
Clinical Features
Diagnosis
Course, Prognosis and Treatment
Salient Features
Gianotti-Crosti Syndrome
Historical Aspects
Epidemiology
Etiology
Pathogenesis
Clinical Features
Differential Diagnosis
Laboratory Investigations
Diagnosis
Treatment
Course and Prognosis
Salient Features
Kawasaki Disease
Definition
Historical Aspects
Etiology
Epidemiology
Pathogenesis
Clinical Features
Laboratory Investigations
Diagnosis
Course, Complications and Prognosis
Treatment
Salient Features
Papular-Purpuric Gloves and Socks Syndrome
Historical Aspects
Etiology
Epidemiology
Clinical Features
Diagnosis
Course, Prognosis and Complications
Salient Features
ACKNOWLEDGEMENT
CHAPTER 10:
Fungal Infections
INTRODUCTION
SUPERFICIAL FUNGAL INFECTIONS
Superficial Mycoses
Dermatophytoses
Etiology
Taxonomy and Nomenclature
Ecology
Epidemiology
Pathogenesis
Clinical Manifestations
Diagnosis
Treatment
Non-dermatophyte Superficial Fungal Infections
Candidal Infections
Etiopathogenesis
Clinical Features
Diagnosis
Treatment
DEEP FUNGAL INFECTIONS
Subcutaneous Fungal Infections
Sporotrichosis
Epidemiology
Clinical Features
Differential Diagnosis
Diagnosis
Treatment
Mycetoma
Epidemiology
Etiology
Clinical Features
Differential Diagnosis
Laboratory Diagnosis
Treatment
Chromoblastomycosis
Epidemiology
Etiology
Clinical Features
Differential Diagnosis
Diagnosis
Treatment
Rhinosporidiosis
Epidemiology
Etiology
Clinical Features
Differential Diagnosis
Diagnosis
Treatment
SYSTEMIC MYCOSIS
Cutaneous Manifestations of Systemic Mycoses
Blastomycosis
Coccidioidomycosis
Histoplasmosis
Paracoccidioidomycosis
OPPORTUNISTIC FUNGAL INFECTIONS
Cryptococcosis
Aspergillosis
Zygomycosis
Mucormycosis
CHAPTER 11:
Sexually Transmitted Infections Including HIV Infection
INTRODUCTION
PREVALENCE
BACTERIAL SEXUALLY TRANSMITTED INFECTIONS
Syphilis
Congenital Syphilis
Acquired Syphilis in Children
Gonorrhea
Chlamydial Infection
Treatment
Ophthalmia Neonatorum
Treatment
Prevention
Bacterial Vaginosis
Other Bacterial Sexually Transmitted Infections
SEXUALLY TRANSMITTED INFECTIONS BY PARASITES
Trichomonal Infection
VIRAL SEXUALLY TRANSMITTED INFECTIONS
Herpes Virus Infection
Cytomegalovirus
Herpes Simplex Virus-Type 2
Human Papilloma Virus Infection
Molluscum Contagiosum
HUMAN IMMUNODEFICIENCY VIRUS INFECTION
Diagnosis of HIV Infection in Children
Clinical Events in Infants and Children with Confirmed HIV Infection
Primary HIV Infection
WHO Clinical Stage 1
WHO Clinical Stage 2
WHO Clinical Stage 3
WHO Clinical Stage 4
Management
Assessment and Management after Confirmed Diagnosis of HIV Infection
Management of some Common Mucocutaneous Opportunistic Infections
Antiretroviral Therapy
Control of HIV Infection in Children: Current Scenario
Immune Reconstitution Inflammatory Syndrome with Treatment of HIV Infection
SUMMARY
CHAPTER 12:
Diseases due to Protozoa and Helminths
INTRODUCTION
PROTOZOAN INFECTIONS
Cutaneous Leishmaniasis
Epidemiology
Clinical Features
Diagnosis
Treatment
HELMINTHIC INFESTATIONS
Nematodes
Ascariasis
Enterobiasis
Hookworm Infestation
Cutaneous Larva Migrans
Filariasis
Cysticercosis
CHAPTER 13:
Bites, Stings and Infestations
BITES
Introduction
Papular Urticaria
Etiology
Histopathology
Clinical Features
Differential Diagnosis
Treatment
Other Reactions to Arthropod Bite and Stings
Order Diptera (Mosquitoes, Flies)
Order Siphonaptera (Fleas)
Order Hymenoptera (Bees, Wasps)
Order Hemiptera (Bugs)
Order Coleoptera (Beetles)
Order Lepidoptera (Butterflies and Moths)
Class Arachnida
Order Araneae (Spiders)
Order Scorpionida (Scorpions)
Order Acarina (Ticks)
Chilopoda and Diplopoda (Centipedes and Millipedes)
OTHER NOXIOUS AND VENOMOUS STINGS
Leeches (Hirudinea)
INJURIES BY AQUATIC CREATURES
Jellyfish, Portuguese Man-of-War, Sea Anemones and Corals
Echinoderms: Sea Urchins, Starfish and Sea Cucumbers
OTHER ANIMAL AND HUMAN BITES
INFESTATIONS
Scabies
Etiopathogenesis
Epidemiology
Clinical Features
Differential Diagnosis
Diagnosis
Treatment
Pediculosis
Etiology
Epidemiology
Clinical Features
Differential Diagnosis
Diagnosis
Treatment
Myiasis
Clinical Features
Treatment
Tungiasis
CHAPTER 14:
Diseases of the Mucous Membranes
INTRODUCTION
MOUTH ULCERS
Recurrent Aphthous Stomatitis
Etiology
Treatment
Behçet's Syndrome
Etiology
Clinical Features
Treatment
Traumatic Ulceration
Infections
Viral
Fungal
Bacterial
Neoplasia
Systemic Diseases
Dermatological Diseases
Lichen Planus/Lichenoid Reactions
Vesiculobullous Diseases
Connective Tissue Disorders
WHITE PATCHES
Physiological Lesions
Fordyce's Spots
Epstein's Pearls and Bohn's Nodules
Hereditary Disorders
White Sponge Nevus
Hereditary Benign Intraepithelial Dyskeratosis
Darier's Disease
Pachyonychia Congenita
Dyskeratosis Congenita
Acquired Causes
Frictional (Traumatic) Keratosis
Chemical Injuries
Koplik's Spots
Candidiasis
Hairy Leukoplakia
RED AND PIGMENTED LESIONS
Amalgam Tattoo
Drug-Induced Pigmentation
Peutz-Jeghers Syndrome
Hemangioma
Hereditary Hemorrhagic Telangiectasia
Osler-Weber-Rendu Disease
SWELLINGS/LUMPS
Soft Tissue Swelling
Bony Swellings
Gingival Swelling
Hereditary Gingival Fibromatosis
Gingival Hyperplasia
Salivary Gland Swelling
LESIONS OF THE TONGUE
Congenital Lesions
Acquired Lesions
Glossitis
Infections
Erythema Migrans (Geographic Tongue)
Hairy Tongue
CHAPTER 15:
Disorders of Hair
INTRODUCTION
NORMAL HAIR
Development
Types of Hair
Lanugo Hairs
Vellus Hairs
Terminal Hairs
Density, Distribution and Growth Rate of Hair
Structure of Hair
Hair Cycle
Anagen
Catagen
Telogen
Neonatal Hair
Disorders of Hair
CONGENITAL OR EARLY ONSET ALOPECIA
Congenital Diffuse Alopecia
Hypotrichosis Occurring Alone or with Other Minor Abnormalities
Hypotrichosis with Ectodermal Dysplasias
Hypotrichosis with Ichthyoses
Hypotrichosis with Premature Aging Syndromes
Hypotrichosis with Immunodeficiency Syndromes
Hypotrichosis with Genetic Disorders of the Hair Shaft
Congenital Localized Alopecia
Neonatal Occipital Alopecia
Birth Injury on Scalp
Temporal Triangular Alopecia
Localized Alopecia Associated with Other Nevoid Conditions
Hypotrichosis with Congenital Forms of Cutis Verticis Gyrata
Localized Alopecia Associated with Syndromes
X-Linked Dominant Conditions
NONSCARRING ALOPECIA
Telogen Effluvium
Anagen Effluvium
Alopecia Areata
Etiopathogenesis
Clinical Features
Diagnosis and Differential Diagnosis
Course and Prognosis
Management
Androgenetic Alopecia
Traumatic Alopecia
Traction Alopecia
Trichotillomania
Loose Anagen Hair
Hair Shaft Disorders
Hair Shaft Abnormalities with Increased Fragility
Trichorrhexis Invaginata
Trichothiodystrophy
Hair Shaft Abnormalities without Increased Hair Fragility
SCARRING ALOPECIA
Keratosis Pilaris Atrophicans
Keratosis Pilaris Atrophicans Faciei (Ulerythema Ophryogenes)
Atrophoderma Vermiculatum
Keratosis Follicularis Spinulosa Decalvans of Siemens
Folliculitis Decalvans
Dissecting Cellulitis of the Scalp
Acne Keloidalis
Pseudopelade
Alopecia Mucinosa
HYPERTRICHOSIS
Diffuse Hypertrichosis
Primary Hypertrichosis
Hypertrichosis As Part of Other Genetically Determined Disorders
Drug-Induced Hypertrichosis
Localized Hypertrichosis
Nevoid Hypertrichosis
Hypertrichosis Cubiti
Anterior Cervical Hypertrichosis
Posterior Cervical Hypertrichosis
Lumbosacral Hypertrichosis or Faun Tail Deformity
Hypertrichosis with Cranial Meningoceles, Encephaloceles and Heterotopic Meningeal or Brain Tissue
Hairy Cutaneous Malformations of Palms and Soles
Scrotal Hair
Hypertrichosis with Focal Facial Dermal Dysplasia
Hemihypertrophy with Hypertrichosis
Localized Hypertrichosis in Association with Nevi or Tumors
Hypertrichosis Due to Local Heat and Cutaneous Hyperemia
Management of Hypertrichosis
Bleaching
Trimming
Physical Depilation
Chemical Depilatories
Electrolysis
Laser Therapy and Intense Pulsed Light Therapy
Eflornithine Hydrochloride
HIRSUTISM
Pathogenesis
Classification
Clinical Features
Diagnosis
Treatment
ERUPTIVE VELLUS HAIR CYSTS
ABNORMALITIES OF HAIR COLOR
Diffuse Hypopigmentation of Hair
Primary Diffuse Hypopigmentation of Hair
Premature Graying (Canities)
Acquired Reversible Diffuse Hypopigmentation
Localized Hypopigmentation of Hair (Poliosis)
ALTERED PIGMENTATION OF HAIR DUE TO EXOGENOUS AGENTS
Drugs
Chemicals
CHAPTER 16:
Disorders of Nail
INTRODUCTION
ANATOMY
PATHOLOGICAL CHANGES OF THE NAIL APPARATUS
Alterations in the Nail Plate
Onychomadesis
Washboard Nails
Pitting
Multiple Longitudinal Nail Grooves
Onychauxis
Alterations in the Nail Bed
Alterations in Nail Size
Anonychia/Micronychia
Polyonychia
Alteration in Nail Contour
Alteration in Nail Color
Acquired
Hereditary
Alteration in Growth Rate
TRAUMATIC NAIL DISORDERS
Nail-Biting and Onychotillomania
PARONYCHIA
LEUKONYCHIA
NAIL CHANGES IN PRIMARY CUTANEOUS DISORDERS
Eczema
Lichen Planus
Psoriasis
Twenty-Nail Dystrophy
Warts
NAIL CHANGES IN GENODERMATOSES
Epidermolysis Bullosa
Pachyonychia Congenita
Yellow Nail Syndrome
Nail Patella Syndrome
Ectodermal Dysplasias
Tuberous Sclerosis
Trichothiodystrophy
Porphyrias
NAIL CHANGES IN SYSTEMIC DISORDERS
Koilonychia
Clubbing
Shell Nails
Mees’ Lines
Muehrcke's Lines
Lindsay's Nails
Terry's Nails
Specific Nail Changes in Cardiopulmonary Diseases
Nail Changes in Endocrine and Rheumatologic Diseases
NAIL CHANGES ASSOCIATED WITH CHEMOTHERAPY IN CHILDREN
CHAPTER 17:
Disorders of Cutaneous Appendages
DISORDERS OF SEBACEOUS GLANDS
Anatomy and Physiology of Sebaceous Glands
Acne
Clinical Features
Differential Diagnosis
Treatment
Management of Acne Scarring
Acne Variants
Neonatal, Infantile and Juvenile Acne
Drug-Induced Acne
Acne Excoriee
Acne Fulminans
Acne Conglobata
Gram-Negative Folliculitis
Other Disorders Related to Acne
Hyperandrogenism
Steatocystoma Multiplex
Childhood Rosacea
DISORDERS OF ECCRINE SWEAT GLANDS
Anatomy and Physiology of Human Eccrine Glands
Classification of Eccrine Sweat Gland Disorders
Hyperhidrosis
Hypohidrosis or Anhidrosis
Sweat Retention Syndromes
Chemotherapy-Associated Eccrine Reactions
Hyperhidrosis
Anhidrosis
Miliaria
Eccrine Bromhidrosis
Neutrophilic Eccrine Hidradenitis
Granulosis Rubra Nasi
DISORDERS OF APOCRINE GLANDS
Apocrine Bromhidrosis (Osmidrosis)
Apocrine Chromhidrosis
Apocrine Miliaria (Fox-Fordyce Disease)
Hidradenitis Suppurativa
Tumors
CHAPTER 18:
Childhood Psoriasis
INTRODUCTION
ETIOLOGY AND PATHOGENESIS
HISTOPATHOLOGY
CLINICAL FEATURES
Epidemiological Data
Clinical Variants of Psoriasis in Children
Plaque Psoriasis
Guttate Psoriasis
Flexural Psoriasis
Pustular Psoriasis
Erythrodermic Psoriasis
Nail Involvement
Psoriatic Diaper Rashes
Eczema/Psoriasis Overlap
Congenital Psoriasis
DIFFERENTIAL DIAGNOSIS
COMORBIDITIES
QUALITY OF LIFE
LONG-TERM BEHAVIOR OF CHILDHOOD PSORIASIS INTO ADULTHOOD
TREATMENT
Avoidance/Removal of Triggering Factors
Topical Therapy
Phototherapy
Systemic Therapy
Indications
CHAPTER 19:
Erythroderma in Children
INTRODUCTION
EPIDEMIOLOGY
CAUSES AND CLINICAL FEATURES OF ERYTHRODERMA
APPROACH TO A CHILD WITH ERYTHRODERMA
MANAGEMENT OF CHILDHOOD ERYTHRODERMA
CHAPTER 20:
Lichen Planus, Lichenoid Disorders and other Papulosquamous Disorders
INTRODUCTION
LICHEN PLANUS
Epidemiology
Etiopathogenesis
Clinical Features
Differential Diagnosis
Laboratory Investigations
Treatment
Course and Prognosis
LICHENOID DISORDERS
Lichen Nitidus
Epidemiology
Etiopathogenesis
Clinical Features
Differential Diagnosis
Diagnosis
Treatment
Lichen Striatus
Epidemiology
Etiopathogenesis
Clinical Features
Differential Diagnosis
Diagnosis
Treatment
Pityriasis Lichenoides
Epidemiology
Etiopathogenesis
Clinical Features
Differential Diagnosis
Diagnosis
Treatment
OTHER SKIN DISEASES WITH LICHENOID ERUPTIONS
Graft Versus Host Disease
Frictional Lichenoid Eruption
OTHER PAPULOSQUAMOUS DISORDERS
Pityriasis Rosea
Epidemiology
Etiopathogenesis
Clinical Features
Differential Diagnosis
Diagnosis
Histopathology
Treatment
Pityriasis Rubra Pilaris
Epidemiology
Etiopathogenesis
Classification
Clinical Features
Differential Diagnosis
Diagnosis
Treatment
Parapsoriasis
Epidemiology
Etiopathogenesis
Clinical Features
Differential Diagnosis
Diagnosis
Treatment
CHAPTER 21:
Vesiculobullous Disorders
INTRODUCTION
IMMUNOBULLOUS DISORDERS
Classification
Intraepidermal Bullous Disorders
Pemphigus
Subepidermal Bullous Disorders
Pemphigoid
Dermatitis Herpetiformis
Chronic Bullous Disease of the Childhood
Epidermolysis Bullosa Acquisita
Bullous Systemic Lupus Erythematosus
MECHANOBULLOUS DISORDERS
Classification
Clinical Types
Epidermolysis Bullosa Simplex
Junctional Epidermolysis Bullosa
Dystrophic Epidermolysis Bullosa
Complications
Differential Diagnosis
Investigations
Management
General Measures
Care of Wound
Surgical Intervention
Specific Therapy
Multidisciplinary Approach
Counseling
CHAPTER 22:
Childhood Vitiligo
INTRODUCTION
EPIDEMIOLOGY
ETIOPATHOGENESIS
CLASSIFICATION OF VITILIGO
Nordlund Classification
Hann Classification of Facial Segmental Vitiligo
CLINICAL FEATURES
Ocular Lesions
ASSOCIATIONS OF VITILIGO
Syndromes Associated with Vitiligo
Vogt-Koyanagi-Harada Syndrome
Alezzandrini Syndrome
APECED Syndrome
COURSE OF VITILIGO
DIFFERENTIAL DIAGNOSIS
Nevus Depigmentosus
Nevus Anemicus
Ash Leaf Macules
Piebaldism
Postinflammatory Hypo/Depigmentation
Pityriasis Versicolor
Leprosy
Contact Vitiligo (Chemical Leukoderma)
DIAGNOSIS
MANAGEMENT
Medical Therapy
Topical Therapy
Systemic Therapy
Phototherapy
Surgical Therapy
Others
Cyclical Therapy
Psychological Support
CHAPTER 23:
Disorders of Pigmentation
INTRODUCTION
CLASSIFICATION
DISORDERS OF HYPERPIGMENTATION
Freckles (Ephelides)
Lentigines
Café Au Lait Macules
Melanocytic Nevi
Congenital Melanocytic Nevi
Acquired Melanocytic Nevi
Dermal Melanocytic Nevi
Childhood Melanoma
Segmental Hypermelanosis
Becker's Nevus
Punctate or Reticulate Pigmentary Disorders
Acquired Hyperpigmentation
DISORDERS OF HYPOPIGMENTATION
Achromic Nevus
Tuberous Sclerosis
Hypomelanosis of Ito
Piebaldism
Oculocutaneous Albinism and other Syndromes with Diffuse Hypomelanosis or Amelanosis
Oculocutaneous Albinism
Chediak-Higashi Syndrome
Phenylketonuria
Ziprkowski-Margolis Syndrome
Acquired Hypopigmentation
Pityriasis Alba
Progressive Macular Hypomelanosis
Lichen Sclerosus et Atrophicus
Pityriasis Versicolor
Postinflammatory Hypopigmentation
Morphea and Scleroderma
Lichen Striatus
Leprosy
Other Conditions
CHAPTER 24:
Photosensitivity and Photodermatoses in Children
INTRODUCTION
ULTRAVIOLET SPECTRUM AND SKIN
ACQUIRED PHOTOSENSITIVITY DERMATOSES
Sunburn
Polymorphous Light Eruptions
Actinic Prurigo (Hydroa Aestivale)
Juvenile Spring Eruptions
Hydroa Vacciniforme
Solar Urticaria
Phototoxic and Photoallergic Reaction
MANAGEMENT
Sun Avoidance
Photoprotection
Sunscreen
CHAPTER 25:
Urticaria, Angioedema and Annular Erythemas
INTRODUCTION
EPIDEMIOLOGY
CLASSIFICATION
ETIOPATHOGENESIS
CLINICAL FEATURES
Spontaneous Urticaria
Physical Urticaria
Dermographism
Pressure Urticaria
Vibratory Urticaria
Cold Urticaria
Cholinergic Urticaria
Solar Urticaria
Contact Urticaria
Hereditary Angioedema
DIFFERENTIAL DIAGNOSIS
LABORATORY INVESTIGATIONS
TREATMENT
ANNULAR ERYTHEMAS
Erythema Annulare Centrifugum
Erythema Marginatum
Erythema Chronicum Migrans
Annular Erythema of Infancy
Differential Diagnosis of Annular Erythemas
CHAPTER 26:
Nevi and Nevoid Disorders
INTRODUCTION
INSIGHT INTO MOSAICISM
Nevi and Heritability
Types of Mosaicism
Clinical Features
Newer Concepts
CLASSIFICATION OF NEVI
NEVOMELANOCYTIC NEVI
Congenital Melanocytic Nevi
Clinical Features
Histopathology
Malignant Potential of Congenital Melanocytic Nevi
Acquired Melanocytic Nevus
Clinical Features
Evolution
Clonality and Tendency to Develop Melanoma
Malignant Potential of Acquired Melanocytic Nevi
Management
Dysplastic Nevi and Atypical Nevi
Atypical Nevi
Dysplastic Nevi
Controversies
Speckled Lentiginous Nevi
Clinical Features
Differential Diagnosis
Histopathology
Treatment
Phakomatosis Pigmentovascularis
Pathogenesis
Differential Diagnosis
Spitz Nevi
Clinical Feature
Differentiation from Melanoma
Histopathology
Treatment
EPIDERMAL NEVI
Classification
Verrucous Epidermal Nevus
Pathogenesis
Histopathology
Management
Inflammatory Linear Verrucous Epidermal Nevus
Pathogenesis
Histopathology
Differential Diagnosis
Treatment
Child Nevus and Child Syndrome
Clinical Features
Pathogenesis
Histopathology
Treatment
Nevus Sebaceous of Jadassohn
Clinical Features
Pathogenesis
Histopathology
Treatment
Nevus Sebaceous Syndromes
Nevus Comedonicus
Clinical Feature
Histopathology
Treatment
Eccrine Nevi
Pure Eccrine Nevi
Eccrine Angiomatous Nevus
Porokeratotic Eccrine Ostial and Dermal Duct Nevus
Apocrine Nevus
Becker's Nevus
Clinical Features
Pathogenesis
Histopathology
Treatment
VASCULAR NEVI
Vascular Malformations
Salmon Patch
Port Wine Stain (Nevus Flammeus)
Syndromes Associated with Port Wine Stain
Sturge-Weber Syndrome
Klippel-Trenaunay Syndrome
Vascular Tumors
Infantile Hemangioma
Congenital Hemangioma
Tufted Angioma
Kaposiform Hemangioendothelioma
Verrucous Hemangioma
Cutis Marmorata Telangiectatica Congenita
NEVUS SYNDROMES
Syndromes with Venous Malformation
Maffucci Syndrome
Blue-Rubber Bleb Nevus Syndrome
Epidermal Nevus Syndrome
Schimmelpenning Syndrome
Phakomatosis Pigmentokeratotica
Proteus Syndrome
Hemihyperplasia Multiple Lipomatosis Syndrome
Becker's Nevus Syndrome
CHAPTER 27:
Neoplastic Disorders of Skin
INTRODUCTION
CLASSIFICATION
NEVI AND HAMARTOMAS
Epidermal Nevi
Keratinocytic Nevi/Hamartomas
Organoid Nevi/Hamartomas
Dermal and Subcutaneous Nevi
Collagen Nevi/Hamartomas
Proteoglycan Nevus/Hamartoma
Fibrous Tissue Nevus/Hamartoma
Muscular Nevi/Hamartoma
Fatty Tissue Nevus/Hamartoma
Vascular Nevi
Vascular Tumors
Melanocytic Nevi
Epidermal Melanocytic Nevi
Dermal Melanocytic Nevi
BENIGN AND MALIGNANT NEOPLASIA
Epidermal Neoplasia
Adnexal Neoplasia
Sebaceous Tumors
Follicular Tumors
Eccrine Tumors
Dermal and Subcutaneous Neoplasia
Fibrous Tumors (Juvenile Fibromatoses)
Fat Tumors
Vascular Neoplasia
Blood Vessel Tumors
Lymphatic Tumors
Melanocytic Neoplasia
Melanoma
SYNDROMES ASSOCIATED WITH CUTANEOUS TUMORS AND TUMOR-LIKE CONDITIONS
CUTANEOUS METASTASES FROM INTERNAL MALIGNANCIES
Cutaneous Metastases from Hematological Malignancies
Leukemia Cutis (Non-congenital)
Congenital Leukemia Cutis
Cutaneous Metastases from Nonhematological Malignancies
Neuroblastoma
Rhabdomyosarcoma
CHAPTER 28:
Disorders of Dermis and Subcutaneous Fat
INTRODUCTION
PANNICULITIS
Classification
Specific Panniculitis in Children
Subcutaneous Fat Necrosis of the Newborn
Sclerema Neonatorum
Cold Panniculitis
Post-Steroid Panniculitis
Adult Type Panniculitis Appearing in Children
Erythema Nodosum
Erythema Induratum of Bazin
Infective Panniculitis
Alpha-1 Antitrypsin Deficiency Panniculitis
Pancreatic Panniculitis
Lupus Panniculitis/Lupus Erythematosus Profundus
Panniculitis due to Polyarteritis Nodosa
Factitial Panniculitis/Artifactual Panniculitis
Subcutaneous Granuloma Annulare
Cytophagic Histiocytic Panniculitis
Idiopathic Lipoatrophic Panniculitis
Idiopathic Palmoplantar Hidradenitis (Plantar Panniculitis)
GRANULOMA ANNULARE
Etiology and Pathogenesis
Histopathology
Clinical Features
Localized GA
Generalized GA
Perforating GA
Subcutaneous GA (Pseudo-rheumatoid Nodule)
Arcuate Dermal Erythema/Patch GA
Differential Diagnosis
Associations
Course
Treatment
LIPODYSTROPHY
Classification
Congenital Lipodystrophy
Acquired Lipodystrophy
Management
FIBROMATOSIS
Classification
Benign Fibromatoses of Childhood
Myofibroma/Myofibromatosis
Fibromatosis Colli
Fibrous Hamartoma of Infancy
Nodular Fasciitis
Fibromatoses with a Locally Aggressive Course
Infantile Fibromatosis
Plantar-Palmar Fibromatosis
Gingival Fibromatosis
Digital (Inclusion Body) Fibromatosis
Calcifying Aponeurotic Fibroma
Giant Cell Fibroblastoma
Juvenile Hyaline Fibromatosis and Infantile Systemic Hyalinosis
CHAPTER 29:
Histiocytosis and Cutaneous Mastocytosis
HISTIOCYTOSIS
Classification
Class I Histiocytosis
Pathogenesis
Clinical Features
Investigations
Course and Prognosis
Differential Diagnosis
Treatment
Class II Histiocytosis
Juvenile Xanthogranuloma
Benign Cephalic Histiocytosis
Generalized Eruptive Histiocytoma
Papular Xanthoma
Xanthoma Disseminatum
Class III Histiocytosis
CUTANEOUS MASTOCYTOSIS
Pathogenesis
Classification
Epidemiology
Clinical Features
Maculopapular Form of Cutaneous Mastocytosis
Nodular Form of Cutaneous Mastocytosis
Telangiectatic Cutaneous Mastocytosis
Diffuse Cutaneous Mastocytosis
Diagnosis
Initial Work-up of a Child with Cutaneous Mastocytosis
Skin Biopsy and Histopathological Examination
Other Investigations
Differential Diagnosis
Treatment and Follow-Up
Course and Prognosis
CHAPTER 30:
Skin in Systemic Diseases
INTRODUCTION
DISORDERS OF GASTROINTESTINAL SYSTEM
Inflammatory Bowel Disease
Pyoderma Gangrenosum
Mucocutaneous Granulomas
Erythema Nodosum
Aphthous Ulcers
Malnutrition
Intestinal Polyposis
Peutz-Jeghers Syndrome
Gardner Syndrome
Bannayan-Riley-Ruvalcaba Syndrome
Cronkhite-Canada Syndrome
Infections
Helicobacter pylori
Entamoeba histolytica
Giardia intestinalis Infestation
Disorders with Malabsorption
Celiac Disease
Tropical Sprue
HEPATIC AND PANCREATIC DISORDERS
Pancreatitis
Hepatic Disorders
Hepatitis and Acute Liver Disease
Chronic Liver Disease
DISORDERS OF CARDIOVASCULAR SYSTEM
General Cutaneous Signs of Cardiac Diseases
Cyanosis
Flushing
Erythema
Clubbing
Splinter Hemorrhage
Inherited Cardiocutaneous Disorders
Multisystem Diseases
Rheumatic Fever
Subacute Bacterial Endocarditis
DISORDERS OF RESPIRATORY SYSTEM
Yellow Nail Syndrome
Cystic Fibrosis
Atopic Diseases
Carcinoid Syndrome
Löffler's Syndrome
Sarcoidosis
RENAL DISORDERS
Chronic Renal Failure
Xerosis
Hair Changes
Pigmentary Changes
Nail Changes
Vascular Changes
Pruritus
Perforating Disorders
Calcification and Calciphylaxis
Nephrogenic Fibrosing Dermopathy
Renocutaneous Syndrome
Fabry's Disease
Neurofibromatosis (von Recklinghausen's Disease)
Tuberous Sclerosis Complex
von Hippel-Lindau Syndrome
Arthrogryposis-Renal Dysfunction Cholestasis Syndrome
CHILD Syndrome
Nail-Patella Syndrome (Fong Syndrome/Hereditary Onychodysplasia)
Sensenbrenner Syndrome (Cranioectodermal Dysplasia)
Oral-Facial-Digital Syndrome
HEMATOLOGICAL DISORDERS
Dyskeratosis Congenita
Chédiak-Higashi Syndrome
Hermansky-Pudlak Syndrome
Griscelli Syndrome
Fanconi's Anemia
ENDOCRINE DISORDERS
Disorders of Thyroid Gland
Hyperthyroidism
Hypothyroidism
Disorders of Parathyroid Gland
Disorders of Adrenal Gland
Cushing's Syndrome
Addison's Disease
Disorders of Pituitary Gland
Hyperpituitarism
Hypopituitarism
Disorders Associated with Androgen Excess
Congenital Adrenal Hyperplasia (Adrenogenital Syndrome)
Polycystic Ovary Syndrome (Stein-Leventhal Syndrome)
Cutaneous Manifestations of Diabetes Mellitus
Necrobiosis Lipoidica Diabeticorum
Diabetic Dermopathy
Diabetic Bullae
Acanthosis Nigricans
Syndromes Associated with Multiple Endocrine Gland Dysfunctions
Multiple Endocrine Neoplasia Syndromes
PSYCHOCUTANEOUS DISORDERS
Psychological Importance of Skin
Psychocutaneous Disorders Encountered in Children
Body Dysmorphic Disorder (Dysmorphophobia, Dermatological Non-disease)
Anorexia Nervosa and Bulimia
Epidemic Hysteria Syndrome
Self-Inflicted and Simulated Skin Disease
Trichotillomania
Onychotillomania and Onychophagia
Dermatitis Artefacta
Factitious Cheilitis
Nail Artefact
Münchausen's Syndrome by Proxy
Hyperhidrosis
Psychogenic Pruritus
CUTANEOUS MANIFESTATIONS OF INTERNAL MALIGNANCIES
Introduction
Direct Tumor Involvement of the Skin
Genetically Determined Syndromes with Increased Predisposition to Malignancy
Cutaneous Paraneoplastic Syndromes
PURPURA FULMINANS
Definition
Classification
Etiopathogenesis
Epidemiology
Clinical Features
Treatment
Course and Prognosis
SARCOIDOSIS
Etiology
Epidemiology
Immunology
Histopathology
Clinical Features
Specific Lesions
Unusual and Atypical Forms
Nail Changes
Mucosal Involvement
Eyes
Uveo-parotid Fever
Skeletal System
Pulmonary Involvement
Diagnosis
Treatment
Topical Therapy
Systemic Therapy
Course
GRAFT-VERSUS-HOST DISEASE
Definition
Acute Graft-versus-Host Disease
Pathogenesis
Clinical Features
Diagnosis
Histopathology
Prognostic Factors
Course
Chronic Cutaneous Graft-versus-Host Disease
Pathogenesis
Histopathology
Treatment
CHAPTER 31:
Collagen Vascular Disorders
INTRODUCTION
DISCOID LUPUS ERYTHEMATOSUS
Epidemiology
Etiopathogenesis
Clinical Features
Course and Prognosis
Diagnosis
Differential Diagnosis
Differentiating Features from Adult Disease
Management
Topical Therapy
Systemic Therapy
SYSTEMIC LUPUS ERYTHEMATOSUS
Epidemiology
Etiopathogenesis
Clinical Features
Cutaneous Manifestations
Systemic Manifestations
Course and Prognosis
Diagnosis
Diagnostic Criteria
Laboratory Investigations
Differential Diagnosis
Differentiating Features from Adult Systemic Lupus Erythematosus
Management
Treatment of Cutaneous Lesions
Treatment of Systemic Involvement
NEONATAL LUPUS ERYTHEMATOSUS
Epidemiology
Etiopathogenesis
Clinical Features
Cutaneous Involvement
Systemic Involvement
Course and Prognosis
Diagnosis
Differential Diagnosis
Management
JUVENILE DERMATOMYOSITIS
Epidemiology
Etiopathogenesis
Clinical Features
Muscle Involvement
Cutaneous Involvement
Amyopathic DM
Systemic Involvement
Course and Prognosis
Diagnosis
Clinical Assessment
Laboratory Evaluation
Imaging
Histopathology
Electromyography
Differential Diagnosis
Differentiating Features from Adult Disease
Management
CHILDHOOD SCLERODERMA
Morphea
Epidemiology
Etiopathogenesis
Clinical Features
Course and Prognosis
Diagnosis
Differential Diagnosis
Differentiating Features from Adult Disease
Management
Systemic Sclerosis
Epidemiology
Etiopathogenesis
Clinical Features
Course and Prognosis
Diagnosis
Investigations
Differential Diagnosis
Differentiating Features from Adult Disease
Management
LICHEN SCLEROSUS ET ATROPHICUS
MIXED CONNECTIVE TISSUE DISEASE
CUTANEOUS MANIFESTATIONS OF OTHER COLLAGEN VASCULAR DISORDERS
Juvenile Idiopathic Arthritis
Still's Disease (Juvenile Rheumatoid Arthritis)
CHAPTER 32:
Cutaneous Vasculitides and Neutrophilic Dermatoses in Children
INTRODUCTION
CLASSIFICATION
SMALL VESSEL VASCULITIS
Henoch-Schönlein Purpura
Pathophysiology
Clinical Features
Course and Prognosis
Diagnosis
Management
Antineutrophil Cytoplasmic Antibody-Positive Vasculitides/Necrotizing Vasculitis
Granulomatosis with Polyangiitis (Formerly Wegener's Granulomatosis)
Churg-Strauss Syndrome/Eosinophilic Granulomatosis with Polyangiitis
Microscopic Polyangiitis
Urticarial Vasculitis
Clinical Features
Diagnosis
Differential Diagnosis
Management
Cryoglobulinemic Vasculitis
Clinical Features
Diagnosis
Management
Acute Hemorrhagic Edema of Infancy (Finkelstein's Disease/Seidlmayer Syndrome/Henoch-Schönlein Purpura of Infancy)
MEDIUM VESSEL VASCULITIS
Childhood Polyarteritis Nodosa
Benign Cutaneous Polyarteritis Nodosa
Kawasaki Disease (Mucocutaneous Lymph Node Syndrome)
Clinical Features
Diagnosis
Differential Diagnosis
Management
BEHÇET'S DISEASE
Clinical Features
Oral Ulcers
Genital Ulcers
Papulopustular Lesions
Other Cutaneous Lesions
Systemic Involvement
Treatment
INTRODUCTION
CLASSIFICATION
SWEET SYNDROME
Clinical Features
Associations/Complications
Differentiating Features from Adult SS
Diagnosis
Histopathology
Diagnostic Criteria
Treatment
PYODERMA GANGRENOSUM
ERYTHEMA ELEVATUM DIUTINUM
NEUTROPHILIC ECCRINE HIDRADENITIS
PERIODIC FEVER SYNDROMES
Majeed Syndrome
Sapho Syndrome
CHAPTER 33:
Nutritional Deficiency Disorders
INTRODUCTION
MICRONUTRIENT DEFICIENCY DISORDERS
Thiamine (Vitamin B1) Deficiency
Causes
Pathogenesis
Clinical Manifestations
Management
Riboflavin (Vitamin B2) Deficiency
Causes
Pathogenesis
Clinical Manifestations
Management
Niacin (Vitamin B3) Deficiency
Causes
Pathogenesis
Clinical Features
Management
Pyridoxine (Vitamin B6) Deficiency
Causes
Pathogenesis
Clinical Features
Management
Cyanocobalamine (Vitamin B12) Deficiency
Causes
Pathogenesis
Clinical Features
Management
Ascorbic Acid (Vitamin C) Deficiency
Causes
Pathogenesis
Clinical Features
Management
Biotin (Vitamin H) Deficiency
Causes
Vitamin A Deficiency
Causes
Clinical Features
Management
Acquired Zinc Deficiency
Iron Deficiency
MACRONUTRIENT DEFICIENCY DISORDERS
Essential Fatty Acid Deficiency
Causes
Pathogenesis
Clinical Features
Management
Protein-Energy Malnutrition
Causes
Pathogenesis
Clinical Features
Management
HERITABLE DISORDERS OF NUTRITIONAL DEFICIENCY
Hereditary Disorder of Biotin Deficiency
Clinical Features
Management
Heritable Disorder of Zinc Deficiency (Acrodermatitis Enteropathica)
Pathogenesis
Clinical Features
Diagnosis
Treatment
Course and Follow-Up
Differential Diagnosis
Hereditary Disorder of Copper Deficiency
Hartnup Disease
NUTRITIONAL DEFICIENCY IN PATIENTS WITH EATING DISORDERS
NUTRITIONAL DEFICIENCY IN CHILDREN WITH OTHER MEDICAL/SURGICAL/CUTANEOUS DISORDERS
CHAPTER 34:
Pruritus in Children
INTRODUCTION
ITCH PATHWAY
Classification
Etiology
CUTANEOUS DISORDERS CAUSING PRURITUS
Atopic Dermatitis
Pathogenesis of Pruritus in Atopic Dermatitis
Aggravating Factors for Pruritus in Atopic Children
Measures to Minimize Pruritus in Atopic Children
Other Dermatitis
Urticaria
Cutaneous Mastocytosis
Insect Bites
Infestations
Scabies
Pediculosis
Enterobiasis
Infections
Fungal Infections
Human Immunodeficiency Virus Infection
Papulosquamous Disorders
Drug Reactions
Photodermatoses
Polymorphous Light Eruption
Actinic Prurigo
Solar Urticaria
Vesiculobullous and Pustular Disorders
Linear IgA Disease of Childhood (Chronic Bullous Disease of Childhood)
Epidermolysis Bullosa
Infantile Acropustulosis
Eosinophilic Pustular Folliculitis of Infancy
Genodermatoses
Ichthyosis Vulgaris
Neutral Lipid Storage Disease with Ichthyosis
Netherton's Syndrome
Sjögren-Larsson Syndrome
CHIME Syndrome
Erythrokeratoderma Variabilis
Darier's Disease
Phenylketonuria
Erythropoietic Protoporphyria
Immunodeficiency Disorders
SYSTEMIC DISORDERS CAUSING PRURITUS
Endocrine and Metabolic Disorders
Diabetes Mellitus (Type I)
Hypothyroidism
Hyperthyroidism
Hypoparathyroidism
Hyperparathyroidism
Hepatic Disorders
Pathogenesis of Pruritus in Biliary Obstruction
Clinical Features
Management
Renal Disorders
Clinical Features
Pathogenesis
Management
Malignancies
Lymphoreticular Neoplasms
Polycythemia Vera
Solid Tumors
Neurological Disorders
Neurofibromatosis
Multiple Sclerosis
Cavernous Hemangiomas (Cavernomas) of the Spinal Cord
CHAPTER 35:
Dermatological Drug Therapy in Children
INTRODUCTION
BASIC PRINCIPLES OF DRUG THERAPY IN CHILDREN
Peculiarities of Pediatric Skin, Pharmacokinetics and Pharmacodynamics: Implications for Pharmacotherapy in Children
GENERAL PRINCIPLES OF TOPICAL THERAPY
Barrier Properties of Skin and Percutaneous Absorption
Role of Vehicle/Base
Dispensing Technique of Topical Medication
TOPICAL DRUG THERAPY IN CHILDREN
Emollients
Antibacterials
Antifungals
Antiviral Agents
Antiparasitic Agents
Corticosteroids
Topical Calcineurin Inhibitors
Vitamin D3 Analogs
Retinoids
Local Anesthetics
Astringents
Protectants
Keratolytics
Coal Tar and Anthralin
Sunscreens
SYSTEMIC DRUG THERAPY IN CHILDREN
Antibacterials
Penicillins
Cephalosporins
Tetracyclines
Macrolides
Co-trimoxazole
Antifungal Drugs
Antiviral Drugs
Antihistamines
Glucocorticosteroids
Cyclosporine
Methotrexate
Azathioprine
Cyclophosphamide
Mycophenolic Acid and Mycophenolate Mofetil
Propranolol
Antimalarials
Colchicine
Dapsone
Retinoids
Gammaglobulin
Interferons
Biological Agents
Phototherapy
ADVERSE CUTANEOUS DRUG REACTIONS: ISSUES IN CHILDREN
Mechanism of Adverse Drug Reactions
SOME IMPORTANT ADVERSE CUTANEOUS DRUG REACTION PATTERNS IN CHILDREN
Mild Drug Reactions
Maculopapular Rash
Fixed Drug Eruption
Erythema Multiforme Minor
Severe Drug Reactions
Drug-induced Urticaria and/or Angioedema
Stevens-Johnson Syndrome-Toxic Epidermal Necrolysis
Drug Hypersensitivity Syndrome
Drug-Induced Anaphylaxis
Serum Sickness Like Reaction
Acute Generalized Exanthematous Pustulosis
CHAPTER 36:
Pediatric Dermatological Emergencies
INTRODUCTION
EPIDEMIOLOGY
CLASSIFICATION
DISEASES CAUSING ACUTE SKIN FAILURE
Acute Skin Failure
Consequences of Acute Skin Failure
Management of Acute Skin Failure
DISEASES WITH/DUE TO UNDERLYING SYSTEMIC ILLNESS
Kawasaki Disease
Diagnosis
Management
Purpura Fulminans
Diagnosis
Management
Urticaria and Angioedema
Diagnosis
Management
Infections
Neonatal Herpes Simplex Infection
Kaposi's Varicelliform Eruption
Neonatal Varicella
Diffuse Cutaneous Mastocytosis
Diagnosis
Management
Sclerema Neonatorum
Diagnosis
Management
LOCALIZED DISEASES
Subcutaneous Infections
Kasabach-Merritt Phenomenon
Diagnosis
Management
CHAPTER 37:
Dermoscopy in Children
INTRODUCTION
DERMOSCOPE
PRINCIPLE OF DERMOSCOPY
APPLICATION OF DERMOSCOPY IN PEDIATRIC DERMATOLOGY
Infections
Molluscum Contagiosum
Warts
Lupus Vulgaris
Leishmaniasis
Infestations
Scabies
Pediculosis
Hair Disorders
Alopecia Areata
Trichotillomania
Congenital Triangular Alopecia
Eruptive Vellus Hair Cysts
Scarring Alopecia
Hair Shaft Disorders
Inflammatory Disorders
Psoriasis
Lichen Planus
Urticaria
Acne
Actinic Porokeratosis
Tumors
Basal Cell Carcinoma
Squamous Cell Carcinoma
Benign Melanocytic Nevi and Melanoma
Dermatofibroma
Actinic Keratosis
Seborrheic Keratosis
Sebaceous Hyperplasia
Vascular Tumors
Pyogenic Granuloma
Infantile Hemangioma
Port Wine Stain
Lymphangioma Circumscriptum
Angiokeratoma
Vascular Malformations
Syndromes in Pediatric Age Group
CHAPTER 38:
Dermatosurgery
INTRODUCTION
INDICATIONS OF DERMATOSURGICAL PROCEDURES IN PEDIATRIC PATIENTS
PREOPERATIVE PREPARATION
ANESTHESIA
VARIOUS DERMATOSURGICAL PROCEDURES
Curettage
Shave Excision
Fusiform or Elliptical Excision
TECHNIQUE OF SUTURING
Placing Deep Absorbable Suture
Placing Skin Suture
ELECTROSURGERY
Electrocautery
High Frequency Electrosurgery
Electrofulguration
Electrodessication
CRYOSURGERY
CYST EXCISION
WOUND DRESSING AND POSTOPERATIVE CARE
Wound Healing
INTRODUCTION
ANESTHESIA
SURGICAL PROCEDURE
Excision and Primary Closure
Split Thickness and Ultrathin Grafting
Suction Blister Grafting
Miniature Punch Grafting
Non-cultured Melanocyte-Keratinocyte Transplantation
Therapeutic Wounding
INDEX
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