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Transesophageal Echocardiography of Congenital Heart Diseases
Poonam Malhotra Kapoor, Sarvesh Pal Singh
CHAPTER 1:
Introduction to TEE for Congenital Heart Disease
INTRODUCTION
INDICATIONS FOR TEE IN PATIENTS WITH CONGENITAL HEART DISEASE
Diagnostic Indications
Aortic Dissection
Perioperative Indications
TEE GUIDED INTERVENTIONS
CONTRAINDICATIONS FOR THE USE OF TEE (TABLE 1)
Absolute
Relative
DEFINITIONS
SIGNIFICANCE
IMAGING PLANES AND ORIENTATION
GOALS OF THE EXAMINATION
PROBE INSERTION
PROBE MANIPULATION
Terminology of TEE Probe Manipulation
ACHD: TRANSESOPHAGEAL ECHOCARDIOGRAPHIC IMAGING ALGORITHM
CHAPTER 2:
Chambers, Valves and Normal Dimensions
LEFT VENTRICULAR MEASUREMENTS (TABLE 2)
Common Pitfalls of LV
RIGHT VENTRICULAR DIMENSIONS (TABLE 6)
Right Ventricular Function (Fig. 3)
NADAS' CRITERIA
Assessment for Presence of Heart Disease in Children
Major Criteria
Minor Criteria
REFERENCE VALUES FOR NORMAL ADULT TRANSESOPHAGEAL ECHOCARDIOGRAPHY MEASUREMENTS
CHAPTER 3:
TEE Views in Congenital Heart Disease
INTRODUCTION
MIDESOPHAGEAL FOUR CHAMBER VIEW
Probe Manipulation
MIDESOPHAGEAL TWO CHAMBER VIEW
Probe Manipulation
MIDESOPHAGEAL BICOMMISSURAL VIEW
Probe Manipulation
MIDESOPHAGEAL LONG-AXIS VIEW
Probe Manipulation
MIDESOPHAGEAL AORTIC VALVE LONG-AXIS VIEW
Probe Manipulation
MIDESOPHAGEAL AORTIC VALVE SHORT-AXIS VIEW
Probe Manipulation
MIDESOPHAGEAL BICAVAL VIEW
Probe Manipulation
MIDESOPHAGEAL DESCENDING THORACIC AORTA LONG-AXIS VIEW
Probe Manipulation
MIDESOPHAGEAL DESCENDING THORACIC AORTA SHORT-AXIS VIEW
Probe Manipulation
MIDESOPHAGEAL ASCENDING AORTA LONG-AXIS VIEW
Probe Manipulation
MIDESOPHAGEAL ASCENDING AORTA SHORT-AXIS VIEW
Probe Manipulation
MIDESOPHAGEAL LEFT ATRIAL APPENDAGE VIEW
Probe Manipulation
MIDESOPHAGEAL MODIFIED BICAVAL VIEW
Probe Manipulation
MIDESOPHAGEAL RIGHT PULMONARY VEIN VIEW
Probe Manipulation
MIDESOPHAGEAL RIGHT VENTRICLE INFLOW-OUTFLOW VIEW
Probe Manipulation
LOWER ESOPHAGEAL CORONARY SINUS VIEW
Probe Manipulation
TRANSGASTRIC VIEWS
PROBE MANIPULATION TO ACHIEVE TRANSGASTRIC VIEWS
TRANSGASTRIC MODIFIED HEPATIC VEIN VIEW
Probe Manipulation
TRANSGASTRIC TWO CHAMBER VIEW
Probe Manipulation
TRANSGASTRIC APICAL SHORT-AXIS VIEW1
Probe Manipulation
TRANSGASTRIC BASAL LONG-AXIS VIEW2
Probe Manipulation
TRANSGASTRIC BASAL SHORT-AXIS VIEW
Probe Manipulation
TRANSGASTRIC MID-PAPILLARY SHORT-AXIS VIEW
Probe Manipulation
TRANSGASTRIC RIGHT VENTRICLE INFLOW-OUTFLOW VIEW
Probe Manipulation
TRANSGASTRIC RIGHT VENTRICLE INFLOW VIEW
Probe Manipulation
TRANSGASTRIC BASAL RIGHT VENTRICLE OUTFLOW VIEW1
DEEP TRANSGASTRIC LONG-AXIS VIEW
Probe Manipulation
UPPER ESOPHAGEAL AORTIC ARCH LONG-AXIS VIEW
Probe Manipulation
UPPER ESOPHAGEAL AORTIC ARCH SHORT-AXIS VIEW
Probe Manipulation
CONCLUSION
CHAPTER 4:
TEE for Atrial Septal Defect
DEFINITION
PATHOPHYSIOLOGY (FIG. 2A)
DIFFERENT TYPES OF ARTERIAL SEPTAL DISEASE (FIGS 2A AND B)
Ostium Secundum (Figs 3 and 4)
Ostium Primum (Table 1 and Flow chart 1)
Coronary Sinus (Unroofed) (Figs 5 and 6)
CLINICAL SYMPTOMS OF ATRIAL SEPTAL DEFECT
Inspection
P2 Loud
Why There is a Click in Atrial Septal Defect?
CLINICAL INVESTIGATIONS
X-ray Chest in Atrial Septal Defect (Figs 8A and B)
ATRIAL SEPTAL DEFECT ECHOCARDIOGRAM
GUIDELINES WHERE PREOPERATIVE TRANSESOPHAGEAL ECHOCARDIOGRAPHY FOR ATRIAL SEPTAL DEFECT IS MUST
PREOPERATIVE ASSESSMENT OF TEE (FIGS 10 TO 20)
ATRIAL SEPTAL ANEURYSMS
ROBOTIC ATRIAL SEPTAL DEFECT CLOSURE
TEE FOR ASD DEVICE CLOSURE (FIGS 21 TO 24)
Precatheter Assessment
During Catheter Insertion
After Device Deployment
3D TEE
TEE FOR MINIMALLY INVASIVE ASD CLOSURE (FIGS 25 TO 28)
Right Thoracotomy (Fig. 29)
During Catheter/Cannula Placement (Table 2)
SVC Cannulation
Femoral Arterial Cannulation (Figs 32A and B)
Transfemoral IVC Cannulation (Figs 33A to C)
Monitoring during MICS ASD with TEE
TEE for Deairing and Weaning (Figs 33 to 36)
Check ECHO for ASD Repair in ME LAX View
POSTDEVICE CLOSURE ASSESSMENT
POSTOPERATIVE TEE ASSESSMENT
TYPES OF 2° ASD AND DEVICE CLOSURE
After Surgical Closure of ASD, TEE is Performed to Confirm
ADVANTAGES OF MINIMALLY INVASIVE CARDIAC SURGERY FOR ASD CLOSURE
SPECTRUM OF MINIMALLY INVASIVE CARDIAC SURGERY
PTMC and ASD (Fig. 41)
QUANTIFICATION OF 3D OVER 2D TEE (SEE FIGS 42 TO 65)
In Older Children
SUMMARY
FUTURE AND CONTROVERSIES
CHAPTER 5:
TEE for Ventricular Septal Defect
INTRODUCTION
TYPES OF VSD
Perimembranous/Infracristal/Subaortic VSD
Subarterial/Supracristal/ Subpulmonary VSD
Inlet VSD
Muscular VSD
CLINICAL FEATURES
CLINICAL EXAMINATIONS
CVS EXAMINATION
Diagnosis
To Summarize
Katz-Wachtel Phenomenon (Fig. 1)
Maladie DE Roger Syndrome
Name the Conditions where you get Precordial Bulge
Restrictive VSD
Nonrestrictive VSD
Surgical Treatment
Juxta-arterial VSD (AR + ASD)
ECG IN VENTRICULAR SEPTIC DEFECT
X-RAY FINDINGS IN VENTRICULAR SEPTAL DEFECT (FIGS 3 AND 4)
TRANSESOPHAGEAL ECHOCARDIOGRAPHY IN VENTRICULAR SEPTAL DEFECT
PREOPERATIVE TEE ASSESSMENT (FIGS 5 TO 21)
POSTOPERATIVE TEE ASSESSMENT: USING SAME VIEWS AS FOR UNREPAIRED VSD (FIG. 22)
TEE FOR VSD DEVICE CLOSURE (FIGS 23 TO 34)
Pre-catheter Assessment2
During Catheter Insertion
After VSD Device Deployment
VENTRICULAR SEPTAL DEFECT COMPLICATIONS
GERBODE VENTRICULAR SEPTAL DEFECT (FIGS 35 AND 36)
CONCLUSION
CHAPTER 6:
TEE for Atrioventricular Septal Defect
INTRODUCTION
CHEST X-RAY: PAV
Partial Atrioventricular Septal Defect
Complete Atrioventricular Septal Defect
ECG (FIG. 3)
TRANSESOPHAGEAL ECHOCARDIOGRAPHY VIEWS
PREOPERATIVE TRANSESOPHAGEAL ECHOCARDIOGRAPHY
Partial Atrioventricular Septal Defect (Figs 6A and B)
Complete Atrioventricular Septal Defect: Associated Commonly with Down's Syndrome (Figs 7 to 10)
Other Features
POSTOPERATIVE TEE ASSESSMENT
FETAL ECHOCARDIOGRAM IN AVSD
COMPLICATIONS
LONG-TERM OUTCOME
CHAPTER 7:
TEE for Pulmonary Stenosis
INTRODUCTION
PATHOPHYSIOLOGY OF PULMONARY STENOSIS
BRANCH PERIPHERAL PULMONIC STENOSIS
CAUSES AND CLINICAL PRESENTATION
INFUNDIBULAR PULMONARY STENOSIS
CLINICAL SIGNS OF PULMONARY STENOSIS
PULMONARY ARTERY AND VEIN STENOSIS
TEE Findings in a Child with Pulmonary Vein Stenosis and Ventricular Septal Defect
WHY IS PULMONARY STENOSIS A CONCERN?
SEVERITY DEFINITIONS OF PULMONARY STENOSIS
TETRALOGY OF FALLOT WITH INFECTIVE ENDOCARDITIS
ETIOLOGY OF MPA ENDOCARDITIS
TEE ASSESSMENT OF PULMONARY STENOSIS
Preoperative Assessment
Doppler Findings
PERIOPERATIVE CARDIOPULMONARY BYPASS (2D ECHOCARDIOGRAPHY FINDINGS)
POSTOPERATIVE PULMONARY STENOSIS ASSESSMENT (SEE FIGS 15 TO 17)
CHAPTER 8:
TEE for Double-Chambered Right Ventricle
INTRODUCTION
NATURAL HISTORY OF DCRV
ASSOCIATED ANOMALIES
TRANSESOPHAGEAL ECHOCARDIOGRAPHY VIEWS OF DCRV
TEE Views for DCRV
ROLE OF ECHOCARDIOGRAPHY IN DIAGNOSING DOUBLE-CHAMBERED RIGHT VENTRICLE IN ADULTS
PREOPERATIVE TEE ASSESSMENT
ELECTROCARDIOGRAM OF DCRV
POSTOPERATIVE TEE ASSESSMENT (FIGS 5 AND 6)
CONCLUSION
CHAPTER 9:
TEE for Patent Ductus Arteriosus
INTRODUCTION
CLINICAL FEATURES OF PATENT DUCTUS ARTERIOSUS
X-RAY
ECG
ROLE OF TEE IN PDA
TEE VIEWS FOR PATENT DUCTUS ARTERIOSUS: FOR SIMULTANEOUS COARCTATION OF AORTA TO BE RULED OUT
PREOPERATIVE TEE ASSESSMENT
POSTOPERATIVE TEE ASSESSMENT
ROLE OF TEE IN PERCUTANEOUS DEVICE CLOSURE OF PDA
ECHO ASSESSMENT FOLLOWING REPAIR USING THE SAME VIEWS AS FOR UNREPAIRED ASD
CONCLUSION AND FUTURE DIRECTIONS
CHAPTER 10:
TEE for Aortic Coarctation
INTRODUCTION
CLINICAL FEATURES OF AORTIC COARCTATION
PHYSIOLOGY
TRANSESOPHAGEAL ECHOCARDIOGRAPHIC EVALUATION
TRANSESOPHAGEAL ECHOCARDIOGRAPHY ASSESSMENT OF AORTIC COARCTATION
MANAGEMENT OF AORTIC COARCTATION
TRANSESOPHAGEAL ECHOCARDIOGRAPHY ASSESSMENT FOLLOWING COARCTATION REPAIR
CHAPTER 11:
TEE for Tetralogy of Fallot
DEFINITION
ETIOLOGY
COMPONENTS OF TOF (FIG. 1)
EMBRYOLOGY
ASSOCIATED ANOMALIES IN TOF
SYNDROMES ASSOCIATED WITH TOF
CYANOTIC SPELLS IN TOF (FLOW CHART 1)
Cyanotic (Hypoxic) Spells
Treatment of Cyanotic Spells
SQUATTING EPISODE
Mechanism
Equivalents for Squatting
CLINICAL FEATURES IN TOF
General Examination
Auscultation in the TOF Patient
Investigations
Palliative Surgeries in TOF
Definite Surgery
COMPLICATIONS
Definite Procedure
Important Points to Remember in TOF
ANESTHESIA CONSIDERATION IN TOF
Tetralogy of Fallot
Palliative Shunts: Concerns
Post-total Correction of TOF: Concerns
Utility of 2D TEE in TOF Intraoperatively
3D TRANSESOPHAGEAL ECHOCARDIOGRAPHY IN TOF
PREOPERATIVE TEE ASSESSMENT (FIGS 5A TO C)
POSTOPERATIVE TEE ASSESSMENT (FIGS 6 TO 13)
CONCLUSION
CHAPTER 12:
TEE for Double-Outlet Right Ventricle
INTRODUCTION
DEFINITION
VARIOUS CRITERIA FOR CLASSIFICATION OF DORV
Types of DORV
OTHER ANOMALIES WITH DORV
AORTIC OVER-RIDE
CHEST X-RAY
ELECTROCARDIOGRAPHY
USE OF TEE IN DORV
TWO-DIMENSIONAL TEE FOR DORV IN TOF (FIG. 5)
Anatomy and Suggested Two-Dimensional Views
Views for RVOT
Color Doppler
VENTRICULAR SEPTAL DEFECT
LOCATION OF VSD IN DORV
PREOPERATIVE ASSESSMENT OF DORV ON TEE (FIG. 5)
ASSESSMENT FOR ROUTABILITY OF VSD (FIG. 6)
ANATOMY AND SUGGESTED TWO-DIMENSIONAL VIEWS FOR ROUTABILITY OF VENTRICULAR SEPTAL DEFECT
POSTOPERATIVE ASSESSMENT OF DORV ON TEE (FIGS 7 TO 9)
CONCLUSION
CHAPTER 13:
TEE for Transposition of Great Arteries
INTRODUCTION
PREOPERATIVE TEE ASSESSMENT
For Arterial Switch Operation
Surgical Options Apart from ASO in Selected Patients (with Severe Pulmonary Stenosis)
Rastelli Procedure
Nikaidoh Operation (Aortic Translocation)
Options for Regressed Left Ventricle
TRANSESOPHAGEAL ECHOCARDIOGRAPHY FOR SENNING PROCEDURE
ASSESSMENT OF THE PULMONARY VENOUS PATHWAY
ASSESSMENT OF SYSTEMIC VENOUS PATHWAY
ASSESSMENT OF BAFFLE
PERIOPERATIVE CARE, POST-SENNING OPERATION
POSTOPERATIVE TEE ASSESSMENT (FIGS 6 TO 24)
CONCLUSION
CHAPTER 14:
TEE for Congenitally Corrected Transposition of Great Arteries
INTRODUCTION
CORRECTED TRANSPOSITION OF GREAT ARTERIES
PREOPERATIVE TEE ASSESSMENT (FIGS 3 TO 19)
POSTOPERATIVE TEE ASSESSMENT
CONCLUSION
CHAPTER 15:
TEE for Ebstein's Anomaly
INTRODUCTION
EMBRYOLOGY
PATHOPHYSIOLOGY
CLINICAL PRESENTATION IN EBSTEIN'S ANOMALY
CLINICAL IMPLICATIONS
ECG IN EBSTEIN'S ANOMALY
X-RAY IN EBSTEIN'S ANOMALY (FIG. 5)
TRANSESOPHAGEAL ECHOCARDIOGRAPHY FOR EBSTEIN'S ANOMALY
ECHOCARDIOGRAPHY OF EBSTEIN'S ANOMALY
TEE Views for Evaluation of Ebstein's Anomaly
PREOPERATIVE TEE ASSESSMENT: 2D AND 3D
Surgical Options for Ebstein's Anomaly
POSTOPERATIVE TEE ASSESSMENT (FIGS 8 TO 11)
KEY POINTS
CHAPTER 16:
TEE for Double-Inlet Left Ventricle
INTRODUCTION
MORPHOLOGY
VENTRICLES
ASSOCIATED ANOMALIES WITH DILV
PATHOPHYSIOLOGY/ NATURAL HISTORY OF DILV
CLINICAL PRESENTATION
TESTS TO DIAGNOSE DILV (TABLE 1)
TRANSESOPHAGEAL ECHOCARDIOGRAPHY OF DILV (FIGS 2 TO 7)
CHAPTER 17:
TEE for Univentricular Heart
INTRODUCTION
MORPHOLOGY (FIGS 1A AND B)
Left Ventricular Type
Right Ventricular Type
Indeterminate Type
ATRIOVENTRICULAR CONNECTIONS
INCIDENCE AND SIGNIFICANCE
UNIVENTRICULAR PHYSIOLOGY
AORTOPULMONARY SHUNT
BIDIRECTIONAL GLENN SHUNT
TOTAL CAVOPULMONARY ANASTOMOSIS
PREOPERATIVE ASSESSMENT (FIG. 2)
Pulmonary Anatomy (PA)
OBSTRUCTION OF ANASTOMOSIS
TEE Detected
ECHOCARDIOGRAPHY OF UNIVENTRICULAR HEART (FIGS 3 TO 11)
CHAPTER 18:
TEE for Total Anomalous Pulmonary Venous Connection
INTRODUCTION
DEFINITION
DARLING'S MODIFICATION OF TYPES OF TAPVC
PATHOPHYSIOLOGY OF TAPVC
Pulmonary Vein Stenosis
Supracardiac Type I (TAPVC)
Cardiac Type—II (TAPVC)
Infracardiac Type—Type III
Mixed Type—Type IV
TOTAL ANOMALOUS PULMONARY VENOUS CONNECTION (SUPRACARDIAC)
X-RAY CHEST PAV IN TAPVC (FIGS 2A AND B)
Shape and Size Character
X-RAY CHEST TAPVC (FIGS 2A AND B)
ECG IN TAPVC (FIG. 3)
ANESTHETIC CONSIDERATION
PREOPERATIVE CONSIDERATION
INTRAOPERATIVE CONSIDERATION
PREOPERATIVE ASSESSMENT OF 2D TEE FOR TAPVC (FIGS 4 TO 6)
On 2D TEE
POSTOPERATIVE TEE ASSESSMENT
3D TEE
3D TEE FOR SURGICAL TECHNIQUE
CONCLUSION
CHAPTER 19:
TEE for Cor Triatriatum
DEFINITION
PATHOPHYSIOLOGY
EMBRYOLOGICAL ORIGIN
INTRAOPERATIVE TEE (FIGS 2 AND 3)
Intraoperative TEE Assessment (Figs 4 and 5)
CONGENITAL CARDIAC LESIONS ASSOCIATED WITH CTS4
DIFFERENTIATION BETWEEN SUPRAMITRAL RING AND COR TRIATRIATUM (FIGS 6A AND B)
CHAPTER 20:
TEE for Left Superior Vena Cava
DEFINITION
PATHOPHYSIOLOGY
IMPORTANCE OF LSVC TO THE CARDIAC SURGEON
IDENTIFICATION
TEE FOR LSVC DIAGNOSIS (FIGS 1 TO 6)
LSVC PRESENCE IN CHD
CHAPTER 21:
TEE for Pulmonary Artery Hypertension
INTRODUCTION
CAUSES OF PULMONARY ARTERY HYPERTENSION
CHEST X-RAY FEATURES OF PAH (FIGS 1A AND B)
Precapillary PAH
Dominant Right Ventricle with Pulmonary Hypertension
ECHOCARDIOGRAPHIC FEATURES IN PULMONARY ARTERIAL HYPERTENSION
PREOPERATIVE 2D TEE ASSESSMENT
EVALUATION WITH COLOR FLOW DOPPLER (TABLE 1)
Estimation of PVR
CONCLUSION
CHAPTER 22:
TEE for Eisenmenger's Syndrome
INTRODUCTION
PATHOPHYSIOLOGY OF EISENMENGER'S SYNDROME
Examination in Eisenmenger's Syndrome
CLINICAL IMPLICATIONS
EISENMENGER'S SYNDROME: A PROGRESSIVE DISEASE
EISENMENGER'S PHYSIOLOGY: CLINICAL ASSESSMENT (FIGS 2A TO C)
CHOICES
Electrocardiography (Fig. 3)
Chest X-ray (Figs 4A to C)
Echocardiography
Exercise Testing with Pulse Oximetry Most Useful
2D ECHO: EISENMENGER'S SYNDROME (FIGS 6A TO D)
Course in Adulthood
DIFFERENT CONGENITAL INTRACARDIAC OR EXTRACARDIAC DEFECTS CAN CAUSE EISENMENGER'S SYNDROME
Following Three Account for 70–80% of Cases: To Rule Out on TEE
Other Congenital Heart Diseases which can Cause Eisenmenger's Syndrome
The Causes of Death in Eisenmenger's Patients
Expected Abnormalities
Effect of Eisenmenger's Syndrome on Pregnancy
Salient Points to be Kept in Mind for the Administration of Safe Anesthesia for Cesarean Section
Drawbacks of Administering General Anesthesia to Parturients with Eisenmenger's Syndrome
ECHO PREDICTORS
CONCLUSION
POINTS TO BE REMEMBER
CHAPTER 23:
TEE for Patent Foramen Ovale
INTRODUCTION
STRUCTURE OF PATENT FORAMEN OVALE
CLINICAL FEATURES OF PATENT FORAMEN OVALE
DETECTION OF A RIGHT-TO-LEFT SHUNT THROUGH A PFO
TRANSESOPHAGEAL ECHOCARDIOGRAM
PREOPERATIVE TEE ASSESSMENT OF PATENT FORAMEN OVALE
POSTOPERATIVE ECHO ASSESSMENT FOLLOWING REPAIR
CHAPTER 24:
TEE for Tricuspid Atresia
INTRODUCTION
DEFINITION
ANATOMY
ETIOLOGY AND CLINICAL FEATURES
CHEST X-RAY OF TRICUSPID ATRESIA
ECG FINDINGS
CASE PRESENTATION (FIGS 2 TO 7)
TEE CONFIRMS THE DIAGNOSIS OF TRICUSPID ATRESIA
CHAPTER 25:
Echo Resources
ECHO RESOURCES
Textbooks
Journals
Key Guidelines
SOCIETIES
American Society of Echocardiography
British Society of Echocardiography
European Association of Cardiovascular Imaging
Indian Association of Cardiovascular Thoracic Anaesthesiologists (IACTA)
WEBSITES
INDEX
TOC
Index
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