About Video

Bobble head doll syndrome is a rare and unique movement disorder found in children. Clinically, it is characterized by a to and fro or side-to-side movement of the head at the frequency of 2 to 3 Hz. It is mostly associated with cystic lesions around the third ventricle, choroid plexus papilloma, aqueductal stenosis, and other rare disorders. Recently, transaqueductal web as a unique pathological lesion has been described by one of the authors (KBB). Cerebellar and pyramidal tract signs, and optic atrophy are often seen. The precise pathophysiology is not known. The primary lesion leads to dilatation of the 3rd ventricle and rhythmic movement of the fluid in the offending cyst may exert pressure upon the diencephalic motor pathways, particularly the thalamus, which transmits signals to the motor cortex. The coordination of movement is therefore, compromised. Alternatively, it can be a kind of ‘learned behavior’, where the shaking of the head is an attempt to relieve the obstruction in order to get rid of the symptoms of the obstruction caused by the aqueductal web.